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. 1983 Jun;46(6):515–520. doi: 10.1136/jnnp.46.6.515

Neurophysiological findings in the hereditary presenile dementia characterised by polycystic lipomembranous osteodysplasia and sclerosing leukoencephalopathy.

H P Hakola, V S Partanen
PMCID: PMC1027441  PMID: 6410004

Abstract

17 patients suffering from the presenile dementia characterised by polycystic lipomenbranous osteodysplasia and sclerosing leukoencephalopathy were studied neurophysiologically. Noteworthy findings were diffuse slowing, the accentuation of 6-8 Hz parasagittal activity, slowing of the dominant occipital rhythm and, in the late phase when 13 of patients got epileptic seizures, there was paroxysmal activity in the EEG.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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