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Journal of Neurology, Neurosurgery, and Psychiatry logoLink to Journal of Neurology, Neurosurgery, and Psychiatry
. 1985 Dec;48(12):1269–1276. doi: 10.1136/jnnp.48.12.1269

Congenital hypomyelinating neuropathy.

Y Harati, I J Butler
PMCID: PMC1028613  PMID: 4087003

Abstract

Two patients with congenital hypomyelinating neuropathy are reported with details of sural nerve pathology. The resemblance of this condition to the hypomyelinating neuropathy of Trembler mice is discussed and the pertinent medical literature reviewed.

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Selected References

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  1. Anderson R. M., Dennett X., Hopkins I. J., Shield L. K. Hypertrophic interstitial polyneuropathy in infancy. Clinical and pathologic features in two cases. J Pediatr. 1973 Apr;82(4):619–624. doi: 10.1016/s0022-3476(73)80587-6. [DOI] [PubMed] [Google Scholar]
  2. Guzzetta F., Ferrière G., Lyon G. Congenital hypomyelination polyneuropathy. Pathological findings compared with polyneuropathies starting later in life. Brain. 1982 Jun;105(Pt 2):395–416. doi: 10.1093/brain/105.2.395. [DOI] [PubMed] [Google Scholar]
  3. Hakamada S., Kumagai T., Hara K., Miyazaki S., Miyazaki K., Watanabe K. Congenital hypomyelination neuropathy in a newborn. Neuropediatrics. 1983 Aug;14(3):182–183. doi: 10.1055/s-2008-1059575. [DOI] [PubMed] [Google Scholar]
  4. Karch S. B., Urich H. Infantile polyneuropathy with defective myelination: an autopsy study. Dev Med Child Neurol. 1975 Aug;17(4):504–511. doi: 10.1111/j.1469-8749.1975.tb03502.x. [DOI] [PubMed] [Google Scholar]
  5. Kasman M., Bernstein L., Schulman S. Chronic polyradiculoneuropathy of infancy. A report of three cases with familial incidence. Neurology. 1976 Jun;26(6 Pt 1):565–573. doi: 10.1212/wnl.26.6.565. [DOI] [PubMed] [Google Scholar]
  6. Kennedy W. R., Sung J. H., Berry J. F. A case of congenital hypomyelination neuropathy. Clinical, morphological, and chemical studies. Arch Neurol. 1977 Jun;34(6):337–345. doi: 10.1001/archneur.1977.00500180031007. [DOI] [PubMed] [Google Scholar]
  7. Livingston R. B., Pfenniger K., Moor H., Akert K. Specialized paranodal and interparanodal glial-axonal junctions in the peripheral and central nervous system: a freeze-etching study. Brain Res. 1973 Aug 17;58(1):1–24. doi: 10.1016/0006-8993(73)90820-2. [DOI] [PubMed] [Google Scholar]
  8. Lyon G. Ultrastructural study of a nerve biopsy from a case of early infantile chronic neuropathy. Acta Neuropathol. 1969;13(2):131–142. doi: 10.1007/BF00687025. [DOI] [PubMed] [Google Scholar]
  9. Moss R. B., Sriram S., Kelts K. A., Forno L. S., Lewiston N. J. Chronic neuropathy presenting as a floppy infant with respiratory distress. Pediatrics. 1979 Oct;64(4):459–464. [PubMed] [Google Scholar]
  10. Ono J., Senba E., Okada S., Abe J., Futagi Y., Shimizu H., Sugita T., Hashimoto S., Yabuuchi H. A case report of congenital hypomyelination. Eur J Pediatr. 1982 May;138(3):265–270. doi: 10.1007/BF00441215. [DOI] [PubMed] [Google Scholar]
  11. Palix C., Coignet J. Un cas de polyneuropathie périphérique neo-natale par amyélinisation. Pediatrie. 1978 Mar;33(2):201–207. [PubMed] [Google Scholar]
  12. Rosenbluth J. Intramembranous particle distribution at the node of Ranvier and adjacent axolemma in myelinated axons of the frog brain. J Neurocytol. 1976 Dec;5(6):731–745. doi: 10.1007/BF01181584. [DOI] [PubMed] [Google Scholar]
  13. Towfighi J. Congenital hypomyelination neuropathy: glial bundles in cranial and spinal nerve roots. Ann Neurol. 1981 Dec;10(6):570–573. doi: 10.1002/ana.410100614. [DOI] [PubMed] [Google Scholar]
  14. Ulrich J., Hirt H. R., Kleihues P., Oberholzer M. Connatal polyneuropathy -- a case with proliferated microfilaments in Schwann cells. Acta Neuropathol. 1981;55(1):39–46. doi: 10.1007/BF00691529. [DOI] [PubMed] [Google Scholar]

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