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. 1989 Dec;52(12):1402–1409. doi: 10.1136/jnnp.52.12.1402

Regional cerebral blood flow by SPECT imaging in Sturge-Weber disease: an aid for diagnosis.

C Chiron 1, C Raynaud 1, N Tzourio 1, C Diebler 1, O Dulac 1, M Zilbovicius 1, A Syrota 1
PMCID: PMC1031599  PMID: 2614436

Abstract

Regional cerebral blood flow (rCBF) was studied using SPECT (single photon emission computed tomography) with 133-Xenon in 13 patients with confirmed Sturge-Weber disease, aged 9 months to 18 years. CT scan, performed at the same time, showed evident cerebral angioma in 10 but not in three. A marked hypoperfused area was found in all patients, ranging from -32% to -72% and of the same location as the CT signs. The hypoperfusion seems to result from post ictal phenomenon as well as from chronic ischaemia. SPECT imaging is therefore a sensitive method for visualising intracranial angioma in Sturge-Weber disease and it provides an aid for diagnosis when a CT scan is not reliable.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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