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. 1989 Mar;52(3):314–319. doi: 10.1136/jnnp.52.3.314

Non familial juvenile distal spinal muscular atrophy of upper extremity.

J B Peiris 1, K N Seneviratne 1, H R Wickremasinghe 1, S B Gunatilake 1, R Gamage 1
PMCID: PMC1032402  PMID: 2926413

Abstract

An uncommon variety of non familial, juvenile onset, spinal muscular atrophy with asymmetric distal upper extremity affection is described. One hundred and two patients with a one to 14 year follow up are analysed. Spinal muscular atrophies with a distal distribution are rare. However, in the past three decades, previously unrecognised varieties of neurogenic muscular atrophy have been described in Asia (Japan, India, Sri Lanka and Singapore) under a variety of names. These provide interesting data for discussion of Asian neurogenic muscular atrophies with distal affection, in the context of diseases of the motor neuron.

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Selected References

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