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. 1982 Jan;66(1):26–30. doi: 10.1136/bjo.66.1.26

Preserved para-arteriole retinal pigment epithelium (PPRPE) in retinitis pigmentosa.

J R Heckenlively
PMCID: PMC1039707  PMID: 7055539

Abstract

Five patients with retinitis pigmentosa (RP) with probable autosomal recessive inheritance have been identified in whom there is relative preservation of retinal pigment epithelium adjacent to and under retinal arterioles despite a panretinal degenerative process. All the patients were hypermetropic, though patients with RP tend to be myopic. This implies that there is a factor associated with retinal arterioles which locally retards the RP process in these patients. It may be appropriate to look for the PPRPE pattern in hypermetropic RP patients.

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Selected References

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  1. Deutman A. F., van Blommestein J. D., Henkes H. E., Waardenburg P. J., Solleveld-van Driest E. Butterfly-shaped pigment dystrophy of the fovea. Arch Ophthalmol. 1970 May;83(5):558–569. doi: 10.1001/archopht.1970.00990030558006. [DOI] [PubMed] [Google Scholar]
  2. FRANCESCHETTI A. A curious affection of the fundus oculi: helicoid peripapillar chorioretinal degeneration. Its relation to pigmentary paravenous chorioretinal degeneration. Doc Ophthalmol. 1962;16:81–110. doi: 10.1007/BF00146721. [DOI] [PubMed] [Google Scholar]
  3. Krill A. E., Archer D., Martin D. Sector retinitis pigmentosa. Am J Ophthalmol. 1970 Jun;69(6):977–987. doi: 10.1016/0002-9394(70)91042-1. [DOI] [PubMed] [Google Scholar]
  4. Merin S., Auerbach E. Retinitis pigmentosa. Surv Ophthalmol. 1976 Mar-Apr;20(5):303–346. doi: 10.1016/s0039-6257(96)90001-6. [DOI] [PubMed] [Google Scholar]
  5. Newsome D. A., Fletcher R. T., Chader G. J. Cyclic nucleotides vary by area in the retina and pigmented epithelium of the human and monkey. Invest Ophthalmol Vis Sci. 1980 Aug;19(8):864–869. [PubMed] [Google Scholar]
  6. O'Donnell F. E., Jr, Welch R. B. Fenestrated sheen macular dystrophy. A new autosomal dominant maculopathy. Arch Ophthalmol. 1979 Jul;97(7):1292–1296. doi: 10.1001/archopht.1979.01020020034007. [DOI] [PubMed] [Google Scholar]
  7. Pearlman J. T., Flood T. P., Seiff S. R. Retinitis pigmentosa without pigment. Am J Ophthalmol. 1976 Apr;81(4):417–419. doi: 10.1016/0002-9394(76)90296-8. [DOI] [PubMed] [Google Scholar]
  8. Pearlman J. T., Kamin D. F., Kopelow S. M., Saxton J. Pigmented paravenous retinochorodial atrophy. Am J Ophthalmol. 1975 Oct;80(4):630–635. doi: 10.1016/0002-9394(75)90393-1. [DOI] [PubMed] [Google Scholar]
  9. SJOGREN H. Dystrophia reticularis laminae pigmentosae retinae, an earlier not described hereditary eye disease. Acta Ophthalmol (Copenh) 1950;28(3):279–295. [PubMed] [Google Scholar]
  10. Sieving P. A., Fishman G. A. Refractive errors of retinitis pigmentosa patients. Br J Ophthalmol. 1978 Mar;62(3):163–167. doi: 10.1136/bjo.62.3.163. [DOI] [PMC free article] [PubMed] [Google Scholar]

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