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. 1984 Oct;68(10):727–731. doi: 10.1136/bjo.68.10.727

Yellowish flecks in Leber's congenital amaurosis.

E Chew, A Deutman, A Pinckers, A Aan de Kerk
PMCID: PMC1040454  PMID: 6477853

Abstract

The fundus abnormalities of Leber's congenital amaurosis are extremely variable, from normal to salt-and-pepper changes to typical retinitis pigmentosa. A less commonly seen appearance is that of multiple, irregular shaped, yellowish white flecks deep in the midperipheral retina in a periarteriolar distribution. The nasal fundus as well as the posterior pole are spared. Such a case is presented along with a four-year follow-up together with the fluorescein angiographic findings. The flecks appear to be specific for this entity.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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