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. 1991 Oct;75(10):619–621. doi: 10.1136/bjo.75.10.619

Persistent superior oblique paresis as a manifestation of familial periodic cerebellar ataxia.

P G Bain 1, G B Larkin 1, D M Calver 1, M D O'Brien 1
PMCID: PMC1042501  PMID: 1954213

Abstract

A brother and sister complained of persistent diplopia due to superior oblique palsies. The cause of their symptoms became apparent when they were diagnosed as having familial periodic cerebellar ataxia (FPCA), a rare autosomal dominant condition. Oral acetazolamide (250 mg twice daily) not only prevented all the periodic symptoms but also relieved their diplopia, which had been present between attacks.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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