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Journal of Medical Genetics logoLink to Journal of Medical Genetics
. 1996 Aug;33(8):716–717. doi: 10.1136/jmg.33.8.716

Genotype-phenotype correlation in von Hippel-Lindau disease: identification of a mutation associated with VHL type 2A.

F Chen 1, L Slife 1, T Kishida 1, J Mulvihill 1, S E Tisherman 1, B Zbar 1
PMCID: PMC1050712  PMID: 8863170

Abstract

A family with von Hippel-Lindau disease (VHL) type 2A has been shown to have a T to C missense mutation at nucleotide 547 of the VHL gene. This gives further support for the proposal to associate the 547 T to C mutation with phenotype VHL 2A.

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Selected References

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