Abstract
A one day old baby who presented with cyanosis was later shown to have an isolated persistent left superior vena cava draining into the left atrium with hypoplastic right superior vena cava. This extremely rare anomaly was diagnosed by cardiac catheterisation at one week. Surgical correction at two weeks, by anastomosis of the innominate vein to the right atrium and by ligation of the left superior vena cava at its junction with the left atrium, was successful. This patient is the youngest case in which successful surgical correction of this isolated anomaly has been reported.
Full text
PDF
Images in this article
Selected References
These references are in PubMed. This may not be the complete list of references from this article.
- Bjerregaard P., Laursen H. B. Persistent left superior vena cava. Incidence, associated congenital heart defects and frontal plane P-wave axis in a paediatric population with congenital heart disease. Acta Paediatr Scand. 1980 Jan;69(1):105–108. doi: 10.1111/j.1651-2227.1980.tb07039.x. [DOI] [PubMed] [Google Scholar]
- Foale R., Bourdillon P. D., Somerville J., Rickards A. Anomalous systemic venous return: recognition by two-dimensional echocardiography. Eur Heart J. 1983 Mar;4(3):186–195. doi: 10.1093/oxfordjournals.eurheartj.a061438. [DOI] [PubMed] [Google Scholar]
- KARNEGIS J. N., WANG Y., WINCHELL P., EDWARDS J. E. PERSISTENT LEFT SUPERIOR VENA CAVA, FIBROUS REMNANT OF THE RIGHT SUPERIOR VENA CAVA AND VENTRICULAR SEPTAL DEFECT. Am J Cardiol. 1964 Oct;14:573–577. doi: 10.1016/0002-9149(64)90045-1. [DOI] [PubMed] [Google Scholar]
- Lenox C. C., Zuberbuhler J. R., Park S. C., Neches W. H., Mathews R. A., Fricker F. J., Bahnson H. T., Siewers R. D. Absent right superior vena cava with persistent left superior vena cava: implications and management. Am J Cardiol. 1980 Jan;45(1):117–122. doi: 10.1016/0002-9149(80)90228-3. [DOI] [PubMed] [Google Scholar]
- Pugliese P., Murzi B., Aliboni M., Eufrate S. Absent right superior vena cava and persistent left superior vena cava. Clinical and surgical considerations. J Cardiovasc Surg (Torino) 1984 Mar-Apr;25(2):134–137. [PubMed] [Google Scholar]