Skip to main content
Journal of the Royal Society of Medicine logoLink to Journal of the Royal Society of Medicine
. 1989;82(Suppl 16):11–20.

A rational approach to the nutritional care of patients with cystic fibrosis.

P R Durie 1, P B Pencharz 1
PMCID: PMC1291914  PMID: 2657050

Full text

PDF
11

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Abernathy R. S. Bulging fontanelle as presenting sign in cystic fibrosis. Vitamin A metabolism and effect on cerebrospinal fluid pressure. Am J Dis Child. 1976 Dec;130(12):1360–1362. doi: 10.1001/archpedi.1976.02120130066013. [DOI] [PubMed] [Google Scholar]
  2. Allan J. D., Mason A., Moss A. D. Nutritional supplementation in treatment of cystic fibrosis of the pancreas. Am J Dis Child. 1973 Jul;126(1):22–26. doi: 10.1001/archpedi.1973.02110190018004. [DOI] [PubMed] [Google Scholar]
  3. Ater J. L., Herbst J. J., Landaw S. A., O'Brien R. T. Relative anemia and iron deficiency in cystic fibrosis. Pediatrics. 1983 May;71(5):810–814. [PubMed] [Google Scholar]
  4. Belli D. C., Levy E., Darling P., Leroy C., Lepage G., Giguère R., Roy C. C. Taurine improves the absorption of a fat meal in patients with cystic fibrosis. Pediatrics. 1987 Oct;80(4):517–523. [PubMed] [Google Scholar]
  5. Bertrand J. M., Morin C. L., Lasalle R., Patrick J., Coates A. L. Short-term clinical, nutritional, and functional effects of continuous elemental enteral alimentation in children with cystic fibrosis. J Pediatr. 1984 Jan;104(1):41–46. doi: 10.1016/s0022-3476(84)80586-7. [DOI] [PubMed] [Google Scholar]
  6. Boland M. P., Stoski D. S., MacDonald N. E., Soucy P., Patrick J. Chronic jejunostomy feeding with a non-elemental formula in undernourished patients with cystic fibrosis. Lancet. 1986 Feb 1;1(8475):232–234. doi: 10.1016/s0140-6736(86)90772-5. [DOI] [PubMed] [Google Scholar]
  7. Buchdahl R. M., Cox M., Fulleylove C., Marchant J. L., Tomkins A. M., Brueton M. J., Warner J. O. Increased resting energy expenditure in cystic fibrosis. J Appl Physiol (1985) 1988 May;64(5):1810–1816. doi: 10.1152/jappl.1988.64.5.1810. [DOI] [PubMed] [Google Scholar]
  8. Castillo R., Landon C., Eckhardt K., Morris V., Levander O., Lewiston N. Selenium and vitamin E status in cystic fibrosis. J Pediatr. 1981 Oct;99(4):583–585. doi: 10.1016/s0022-3476(81)80262-4. [DOI] [PubMed] [Google Scholar]
  9. Chase H. P., Long M. A., Lavin M. H. Cystic fibrosis and malnutrition. J Pediatr. 1979 Sep;95(3):337–347. doi: 10.1016/s0022-3476(79)80504-1. [DOI] [PubMed] [Google Scholar]
  10. Cleghorn G. J., Stringer D. A., Forstner G. G., Durie P. R. Treatment of distal intestinal obstruction syndrome in cystic fibrosis with a balanced intestinal lavage solution. Lancet. 1986 Jan 4;1(8471):8–11. doi: 10.1016/s0140-6736(86)91894-5. [DOI] [PubMed] [Google Scholar]
  11. Congden P. J., Bruce G., Rothburn M. M., Clarke P. C., Littlewood J. M., Kelleher J., Losowsky M. S. Vitamin status in treated patients with cystic fibrosis. Arch Dis Child. 1981 Sep;56(9):708–714. doi: 10.1136/adc.56.9.708. [DOI] [PMC free article] [PubMed] [Google Scholar]
  12. Crozier D. N. Cystic fibrosis: a not-so-fatal disease. Pediatr Clin North Am. 1974 Nov;21(4):935–950. doi: 10.1016/s0031-3955(16)33069-3. [DOI] [PubMed] [Google Scholar]
  13. Daniels L., Davidson G. P., Martin A. J. Comparison of the macronutrient intake of healthy controls and children with cystic fibrosis on low fat or nonrestricted fat diets. J Pediatr Gastroenterol Nutr. 1987 May-Jun;6(3):381–386. doi: 10.1097/00005176-198705000-00014. [DOI] [PubMed] [Google Scholar]
  14. Deren J. J., Arora B., Toskes P. P., Hansell J., Sibinga M. S. Malabsorption of crystalline vitamin B 12 in cystic fibrosis. N Engl J Med. 1973 May 3;288(18):949–950. doi: 10.1056/NEJM197305032881808. [DOI] [PubMed] [Google Scholar]
  15. Durie P. R., Forstner G. G., Gaskin K. J., Moore D. J., Cleghorn G. J., Wong S. S., Corey M. L. Age-related alterations of immunoreactive pancreatic cationic trypsinogen in sera from cystic fibrosis patients with and without pancreatic insufficiency. Pediatr Res. 1986 Mar;20(3):209–213. doi: 10.1203/00006450-198603000-00002. [DOI] [PubMed] [Google Scholar]
  16. Elias E., Muller D. P., Scott J. Association of spinocerebellar disorders with cystic fibrosis or chronic childhood cholestasis and very low serum vitamin E. Lancet. 1981 Dec 12;2(8259):1319–1321. doi: 10.1016/s0140-6736(81)91342-8. [DOI] [PubMed] [Google Scholar]
  17. Farrell P. M., Bieri J. G., Fratantoni J. F., Wood R. E., di Sant'Agnese P. A. The occurrence and effects of human vitamin E deficiency. A study in patients with cystic fibrosis. J Clin Invest. 1977 Jul;60(1):233–241. doi: 10.1172/JCI108760. [DOI] [PMC free article] [PubMed] [Google Scholar]
  18. Farrell P. M., Mischler E. H., Engle M. J., Brown D. J., Lau S. M. Fatty acid abnormalities in cystic fibrosis. Pediatr Res. 1985 Jan;19(1):104–109. doi: 10.1203/00006450-198501000-00028. [DOI] [PubMed] [Google Scholar]
  19. Feigal R. J., Shapiro B. L. Mitochondrial calcium uptake and oxygen consumption in cystic fibrosis. Nature. 1979 Mar 15;278(5701):276–277. doi: 10.1038/278276a0. [DOI] [PubMed] [Google Scholar]
  20. Feigelson J., Girault F., Pecau Y. Gastro-oesophageal reflux and esophagitis in cystic fibrosis. Acta Paediatr Scand. 1987 Nov;76(6):989–990. doi: 10.1111/j.1651-2227.1987.tb17283.x. [DOI] [PubMed] [Google Scholar]
  21. Friedman H. Z., Langman C. B., Favus M. J. Vitamin D metabolism and osteomalacia in cystic fibrosis. Gastroenterology. 1985 Mar;88(3):808–813. doi: 10.1016/0016-5085(85)90156-8. [DOI] [PubMed] [Google Scholar]
  22. Gallo-Torres H. E. Obligatory role of bile for the intestinal absorption of vitamin E. Lipids. 1970 Apr;5(4):379–384. doi: 10.1007/BF02532102. [DOI] [PubMed] [Google Scholar]
  23. Gaskin K. J., Durie P. R., Corey M., Wei P., Forstner G. G. Evidence for a primary defect of pancreatic HCO3-secretion in cystic fibrosis. Pediatr Res. 1982 Jul;16(7):554–557. doi: 10.1203/00006450-198207000-00012. [DOI] [PubMed] [Google Scholar]
  24. Gaskin K. J., Durie P. R., Lee L., Hill R., Forstner G. G. Colipase and lipase secretion in childhood-onset pancreatic insufficiency. Delineation of patients with steatorrhea secondary to relative colipase deficiency. Gastroenterology. 1984 Jan;86(1):1–7. [PubMed] [Google Scholar]
  25. Gibbens D. T., Gilsanz V., Boechat M. I., Dufer D., Carlson M. E., Wang C. I. Osteoporosis in cystic fibrosis. J Pediatr. 1988 Aug;113(2):295–300. doi: 10.1016/s0022-3476(88)80268-3. [DOI] [PubMed] [Google Scholar]
  26. Godson C., Ryan M. P., Brady H. R., Bourke S., FitzGerald M. X. Acute hypomagnesaemia complicating the treatment of meconium ileus equivalent in cystic fibrosis. Scand J Gastroenterol Suppl. 1988;143:148–150. doi: 10.3109/00365528809090236. [DOI] [PubMed] [Google Scholar]
  27. Gracey M., Burke V., Anderson C. M. Assessment of medium-chain triglyceride feeding in infants with cystic fibrosis. Arch Dis Child. 1969 Jun;44(235):401–403. doi: 10.1136/adc.44.235.401. [DOI] [PMC free article] [PubMed] [Google Scholar]
  28. Green C. G., Doershuk C. F., Stern R. C. Symptomatic hypomagnesemia in cystic fibrosis. J Pediatr. 1985 Sep;107(3):425–428. doi: 10.1016/s0022-3476(85)80526-6. [DOI] [PubMed] [Google Scholar]
  29. Gurwitz D., Corey M., Francis P. W., Crozier D., Levison H. Perspectives in cystic fibrosis. Pediatr Clin North Am. 1979 Aug;26(3):603–615. doi: 10.1016/s0031-3955(16)33752-x. [DOI] [PubMed] [Google Scholar]
  30. Heinrich H. C., Bender-Götze C., Gabbe E. E., Bartels H., Oppitz K. H. Absorption of inorganic iron- (59Fe2+) in relation to iron stores in pancreatic exocrine insufficiency due to cystic fibrosis. Klin Wochenschr. 1977 Jun 15;55(12):587–593. doi: 10.1007/BF01490513. [DOI] [PubMed] [Google Scholar]
  31. Houvet D., Clerc M. Considerations relatives a un cas d'anencephalie avec difference foeto-maternelle du phenotype Pi. Clin Chim Acta. 1980 Mar 14;102(1):105–110. doi: 10.1016/0009-8981(80)90439-8. [DOI] [PubMed] [Google Scholar]
  32. Jacob R. A., Sandstead H. H., Solomons N. W., Rieger C., Rothberg R. Zinc status and vitamin A transport in cystic fibrosis. Am J Clin Nutr. 1978 Apr;31(4):638–644. doi: 10.1093/ajcn/31.4.638. [DOI] [PubMed] [Google Scholar]
  33. Komp D. M., Selden R. F., Jr Coagulation abnormalities in cystic fibrosis. Chest. 1970 Nov;58(5):501–503. doi: 10.1378/chest.58.5.501. [DOI] [PubMed] [Google Scholar]
  34. Kraemer R., Rüdeberg A., Hadorn B., Rossi E. Relative underweight in cystic fibrosis and its prognostic value. Acta Paediatr Scand. 1978 Jan;67(1):33–37. doi: 10.1111/j.1651-2227.1978.tb16273.x. [DOI] [PubMed] [Google Scholar]
  35. Levy L. D., Durie P. R., Pencharz P. B., Corey M. L. Effects of long-term nutritional rehabilitation on body composition and clinical status in malnourished children and adolescents with cystic fibrosis. J Pediatr. 1985 Aug;107(2):225–230. doi: 10.1016/s0022-3476(85)80130-x. [DOI] [PubMed] [Google Scholar]
  36. Levy L., Durie P., Pencharz P., Corey M. Prognostic factors associated with patient survival during nutritional rehabilitation in malnourished children and adolescents with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1986 Jan;5(1):97–102. doi: 10.1097/00005176-198601000-00018. [DOI] [PubMed] [Google Scholar]
  37. Mansell A. L., Andersen J. C., Muttart C. R., Ores C. N., Loeff D. S., Levy J. S., Heird W. C. Short-term pulmonary effects of total parenteral nutrition in children with cystic fibrosis. J Pediatr. 1984 May;104(5):700–705. doi: 10.1016/s0022-3476(84)80947-6. [DOI] [PubMed] [Google Scholar]
  38. Pencharz P. B. Energy intakes and low-fat diets in children with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1983;2(3):400–402. [PubMed] [Google Scholar]
  39. Pencharz P., Hill R., Archibald E., Levy L., Newth C. Energy needs and nutritional rehabilitation in undernourished adolescents and young adult patients with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1984;3 (Suppl 1):S147–S153. doi: 10.1097/00005176-198400031-00022. [DOI] [PubMed] [Google Scholar]
  40. Rasmussen M., Michalsen H., Lie S. O., Nilsson A., Petersen L. B., Norum K. R. Intestinal retinol esterification and serum retinol in children with cystic fibrosis. J Pediatr Gastroenterol Nutr. 1986 May-Jun;5(3):397–403. doi: 10.1097/00005176-198605000-00011. [DOI] [PubMed] [Google Scholar]
  41. Rogiers V., Dab I., Crokaert R., Vis H. L. Long chain non-esterified fatty acid pattern in plasma of cystic fibrosis patients and their parents. Pediatr Res. 1980 Sep;14(9):1088–1091. doi: 10.1203/00006450-198009000-00015. [DOI] [PubMed] [Google Scholar]
  42. Rosenstein B. J., Langbaum T. S. Incidence of distal intestinal obstruction syndrome in cystic fibrosis. J Pediatr Gastroenterol Nutr. 1983 May;2(2):299–301. [PubMed] [Google Scholar]
  43. Roy C. C., Darling P., Weber A. M. A rational approach to meeting macro- and micronutrient needs in cystic fibrosis. J Pediatr Gastroenterol Nutr. 1984;3 (Suppl 1):S154–S162. doi: 10.1097/00005176-198400031-00023. [DOI] [PubMed] [Google Scholar]
  44. SHWACHMAN H. Therapy of cystic fibrosis of the pancreas. Pediatrics. 1960 Jan;25:155–163. [PubMed] [Google Scholar]
  45. SPROUL A., HUANG N. GROWTH PATTERNS IN CHILDREN WITH CYSTIC FIBROSIS. J Pediatr. 1964 Nov;65:664–676. doi: 10.1016/s0022-3476(64)80151-7. [DOI] [PubMed] [Google Scholar]
  46. SUNG J. H. NEUROAXONAL DYSTROPHY IN MUCOVISCIDOSIS. J Neuropathol Exp Neurol. 1964 Oct;23:567–583. doi: 10.1097/00005072-196410000-00001. [DOI] [PubMed] [Google Scholar]
  47. Scott R. B., O'Loughlin E. V., Gall D. G. Gastroesophageal reflux in patients with cystic fibrosis. J Pediatr. 1985 Feb;106(2):223–227. doi: 10.1016/s0022-3476(85)80291-2. [DOI] [PubMed] [Google Scholar]
  48. Shepherd R. W., Holt T. L., Thomas B. J., Kay L., Isles A., Francis P. J., Ward L. C. Nutritional rehabilitation in cystic fibrosis: controlled studies of effects on nutritional growth retardation, body protein turnover, and course of pulmonary disease. J Pediatr. 1986 Nov;109(5):788–794. doi: 10.1016/s0022-3476(86)80695-3. [DOI] [PubMed] [Google Scholar]
  49. Shepherd R. W., Holt T. L., Vasques-Velasquez L., Coward W. A., Prentice A., Lucas A. Increased energy expenditure in young children with cystic fibrosis. Lancet. 1988 Jun 11;1(8598):1300–1303. doi: 10.1016/s0140-6736(88)92119-8. [DOI] [PubMed] [Google Scholar]
  50. Shepherd R., Cooksley W. G., Cooke W. D. Improved growth and clinical, nutritional, and respiratory changes in response to nutritional therapy in cystic fibrosis. J Pediatr. 1980 Sep;97(3):351–357. doi: 10.1016/s0022-3476(80)80180-6. [DOI] [PubMed] [Google Scholar]
  51. Sitrin M. D., Lieberman F., Jensen W. E., Noronha A., Milburn C., Addington W. Vitamin E deficiency and neurologic disease in adults with cystic fibrosis. Ann Intern Med. 1987 Jul;107(1):51–54. doi: 10.7326/0003-4819-107-1-51. [DOI] [PubMed] [Google Scholar]
  52. Solomons N. W., Wagonfeld J. B., Rieger C., Jacob R. A., Bolt M., Horst J. V., Rothberg R., Sandstead H. Some biochemical indices of nutrition in treated cystic fibrosis patients. Am J Clin Nutr. 1981 Apr;34(4):462–474. doi: 10.1093/ajcn/34.4.462. [DOI] [PubMed] [Google Scholar]
  53. Stutts M. J., Knowles M. R., Gatzy J. T., Boucher R. C. Oxygen consumption and ouabain binding sites in cystic fibrosis nasal epithelium. Pediatr Res. 1986 Dec;20(12):1316–1320. doi: 10.1203/00006450-198612000-00026. [DOI] [PubMed] [Google Scholar]
  54. Thet L. A., Alvarez H. Effect of hyperventilation and starvation on rat lung mechanics and surfactant. Am Rev Respir Dis. 1982 Aug;126(2):286–290. doi: 10.1164/arrd.1982.126.2.286. [DOI] [PubMed] [Google Scholar]
  55. Underwood B. A., Denning C. R. Blood and liver concentrations of vitamins A and E in children with cystic fibrosis of the pancreas. Pediatr Res. 1972 Jan;6(1):26–31. doi: 10.1203/00006450-197201000-00004. [DOI] [PubMed] [Google Scholar]
  56. Vaisman N., Pencharz P. B., Corey M., Canny G. J., Hahn E. Energy expenditure of patients with cystic fibrosis. J Pediatr. 1987 Oct;111(4):496–500. doi: 10.1016/s0022-3476(87)80107-5. [DOI] [PubMed] [Google Scholar]
  57. Walters T. R., Koch H. F. Hemorrhagic diathesis and cystic fibrosis in infancy. Am J Dis Child. 1972 Nov;124(5):641–642. doi: 10.1001/archpedi.1972.02110170019002. [DOI] [PubMed] [Google Scholar]
  58. Weizman Z., Forstner G. G., Gaskin K. J., Kopelman H., Wong S., Durie P. R. Bentiromide test for assessing pancreatic dysfunction using analysis of para-aminobenzoic acid in plasma and urine. Studies in cystic fibrosis and Shwachman's syndrome. Gastroenterology. 1985 Sep;89(3):596–604. doi: 10.1016/0016-5085(85)90456-1. [DOI] [PubMed] [Google Scholar]
  59. Zentler-Munro P. L., Fine D. R., Batten J. C., Northfield T. C. Effect of cimetidine on enzyme inactivation, bile acid precipitation, and lipid solubilisation in pancreatic steatorrhoea due to cystic fibrosis. Gut. 1985 Sep;26(9):892–901. doi: 10.1136/gut.26.9.892. [DOI] [PMC free article] [PubMed] [Google Scholar]

Articles from Journal of the Royal Society of Medicine are provided here courtesy of Royal Society of Medicine Press

RESOURCES