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Journal of the Royal Society of Medicine logoLink to Journal of the Royal Society of Medicine
. 2004;97(Suppl 44):60–71.

Potential benefits of the UK Cystic Fibrosis Database.

G Mehta 1, E J Sims 1, F Culross 1, J D McCormick 1, A Mehta 1
PMCID: PMC1308802  PMID: 15239297

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Corey M., McLaughlin F. J., Williams M., Levison H. A comparison of survival, growth, and pulmonary function in patients with cystic fibrosis in Boston and Toronto. J Clin Epidemiol. 1988;41(6):583–591. doi: 10.1016/0895-4356(88)90063-7. [DOI] [PubMed] [Google Scholar]
  2. Dodge J. A., Morison S., Lewis P. A., Coles E. C., Geddes D., Russell G., Littlewood J. M., Scott M. T. Incidence, population, and survival of cystic fibrosis in the UK, 1968-95. UK Cystic Fibrosis Survey Management Committee. Arch Dis Child. 1997 Dec;77(6):493–496. doi: 10.1136/adc.77.6.493. [DOI] [PMC free article] [PubMed] [Google Scholar]
  3. Farrell P. M., Kosorok M. R., Rock M. J., Laxova A., Zeng L., Lai H. C., Hoffman G., Laessig R. H., Splaingard M. L. Early diagnosis of cystic fibrosis through neonatal screening prevents severe malnutrition and improves long-term growth. Wisconsin Cystic Fibrosis Neonatal Screening Study Group. Pediatrics. 2001 Jan;107(1):1–13. doi: 10.1542/peds.107.1.1. [DOI] [PubMed] [Google Scholar]
  4. Fogarty A., Hubbard R., Britton J. International comparison of median age at death from cystic fibrosis. Chest. 2000 Jun;117(6):1656–1660. doi: 10.1378/chest.117.6.1656. [DOI] [PubMed] [Google Scholar]
  5. Groman Joshua D., Meyer Michelle E., Wilmott Robert W., Zeitlin Pamela L., Cutting Garry R. Variant cystic fibrosis phenotypes in the absence of CFTR mutations. N Engl J Med. 2002 Aug 8;347(6):401–407. doi: 10.1056/NEJMoa011899. [DOI] [PubMed] [Google Scholar]
  6. McCormick Jonathan, Green Michael W., Mehta Gita, Culross Frank, Mehta Anil. Demographics of the UK cystic fibrosis population: implications for neonatal screening. Eur J Hum Genet. 2002 Oct;10(10):583–590. doi: 10.1038/sj.ejhg.5200850. [DOI] [PubMed] [Google Scholar]
  7. Mehta A. Further comments on fibrosing colonpathy study. Lancet. 2001 Nov 3;358(9292):1546–1548. doi: 10.1016/s0140-6736(01)06593-x. [DOI] [PubMed] [Google Scholar]
  8. Mekus F., Ballmann M., Bronsveld I., Dörk T., Bijman J., Tümmler B., Veeze H. J. Cystic-fibrosis-like disease unrelated to the cystic fibrosis transmembrane conductance regulator. Hum Genet. 1998 May;102(5):582–586. doi: 10.1007/s004390050744. [DOI] [PubMed] [Google Scholar]
  9. Ratjen Felix, Döring Gerd. Cystic fibrosis. Lancet. 2003 Feb 22;361(9358):681–689. doi: 10.1016/S0140-6736(03)12567-6. [DOI] [PubMed] [Google Scholar]
  10. Robson M., Abbott J., Webb K., Dodd M., Walsworth-Bell J. A cost description of an adult cystic fibrosis unit and cost analyses of different categories of patients. Thorax. 1992 Sep;47(9):684–689. doi: 10.1136/thx.47.9.684. [DOI] [PMC free article] [PubMed] [Google Scholar]
  11. Rosenstein Beryl J. Nonclassic cystic fibrosis: a clinical conundrum. Pediatr Pulmonol. 2003 Jul;36(1):10–12. doi: 10.1002/ppul.10286. [DOI] [PubMed] [Google Scholar]
  12. Waters D. L., Wilcken B., Irwing L., Van Asperen P., Mellis C., Simpson J. M., Brown J., Gaskin K. J. Clinical outcomes of newborn screening for cystic fibrosis. Arch Dis Child Fetal Neonatal Ed. 1999 Jan;80(1):F1–F7. doi: 10.1136/fn.80.1.f1. [DOI] [PMC free article] [PubMed] [Google Scholar]

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