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. 1992 Oct;33(10):1430–1432. doi: 10.1136/gut.33.10.1430

Sclerosing cholangitis associated with multifocal fibrosis: a case report.

R D Laitt 1, S G Hubscher 1, J A Buckels 1, S Darby 1, E Elias 1
PMCID: PMC1379620  PMID: 1446876

Abstract

The association of sclerosing cholangitis, retroperitoneal fibrosis, and Riedel's thyroiditis has been reported twice before, and on both occasions the authors successfully used steroids to control the fibrotic process. A further case of fibrosis with this triad of organ involvement in which a combination of surgery and steroid treatment has arrested disease progression is described. This suggests an inappropriate immune response in this type of fibrotic overlap syndrome.

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Selected References

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