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. 1977 May;185(5):565–573. doi: 10.1097/00000658-197705000-00009

Periampullary malignancy in Gardner's syndrome.

T R Jones, F C Nance
PMCID: PMC1396157  PMID: 856075

Abstract

Three cases of familial polyposis coli with associated periampullary malignancies are reported and the literature reviewed, which disclosed 16 additional cases. An additional five unreported cases are known to exist. The authors believe that the development of periampullary malignancy in FPC is a definite extracolonic manifestation of the disease and should be considered a variant of Gardner's syndrome. It is recommended that all FPC patients with colon polyps undergo routine surveillance of the upper gastrointestinal tract and that all duodenal polyps discovered be surgically removed when feasible.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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