Skip to main content
PMC home page
Archives of Disease in Childhood logoLink to Archives of Disease in Childhood
. 1977 May;52(5):383–385. doi: 10.1136/adc.52.5.383

Congenital abnormalities associated with extrahepatic portal hypertension.

M Odièvre, G Pigé, D Alagille
PMCID: PMC1544565  PMID: 869567

Abstract

Congenital abnormalities were present in 12 out of 30 (40%) children with extrahepatic portal hypertension of unknown cause, but in only 2 out of 17 (12%) children with extnahepatic portal hypertension secondary to umbilical vein catheterization or omphalitis. The most frequent abnormalities in this series and in published reports were atrial septal defect, malformation of the biliary tract, and anomalous inferior vena cava. These findings are consistent with the view that some cases with extrahepatic portal hypertension are congenital in origin.

Full text

PDF
383

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. CLATWORTHY H. W., Jr, BOLES E. T., Jr Extrahepatic portal bed block in children: pathogenesis and treatment. Ann Surg. 1959 Sep;150:371–383. doi: 10.1097/00000658-195909000-00005. [DOI] [PMC free article] [PubMed] [Google Scholar]
  2. Esposito G. Cavernome portal associé à l'agénésie du rein gauche. Ann Chir Infant. 1966 Jun;7(2):101–106. [PubMed] [Google Scholar]
  3. Fonkalsrud E. W., Myers N. A., Robinson M. J. Management of extrahepatic portal hypertension in children. Ann Surg. 1974 Oct;180(4):487–493. doi: 10.1097/00000658-197410000-00014. [DOI] [PMC free article] [PubMed] [Google Scholar]
  4. HSIA D. Y. Y., GELLIS S. S. Portal hypertension in infants and children. AMA Am J Dis Child. 1955 Sep;90(3):290–291. doi: 10.1001/archpedi.1955.04030010292011. [DOI] [PubMed] [Google Scholar]
  5. Keighley M. R., Girdwood R. W., Wooler G. H., Ionescu M. I. Long-term results of surgical treatment for bleeding oesophageal varices in children with portal hypertension. Br J Surg. 1973 Aug;60(8):641–646. doi: 10.1002/bjs.1800600816. [DOI] [PubMed] [Google Scholar]
  6. LAMY M., JAMMET M. L., NEZELOF C., GUIBERT C. [Studies and reflections on splenoportal thromboses in children]. Arch Fr Pediatr. 1961 Feb;18:182–193. [PubMed] [Google Scholar]
  7. Moretti G., Staeffen J., Broustet A., Le Bras M. Les malformations congénitales associées a la sténose de la veine porte. Sem Hop. 1968 Mar 14;44(13):893–897. [PubMed] [Google Scholar]
  8. Myers N. A., Robinson M. J. Extrahepatic portal hypertension in children. J Pediatr Surg. 1973 Aug;8(4):467–473. doi: 10.1016/0022-3468(73)90208-x. [DOI] [PubMed] [Google Scholar]
  9. Pinkerton J. A., Holcomb G. W., Jr, Foster J. H. Portal hypertension in childhood. Ann Surg. 1972 Jun;175(6):870–886. doi: 10.1097/00000658-197206010-00007. [DOI] [PMC free article] [PubMed] [Google Scholar]
  10. Raffensperger J. G., Shkolnik A. A., Boggs J. D., Swenson O. Portal hypertension in children. Arch Surg. 1972 Aug;105(2):249–254. doi: 10.1001/archsurg.1972.04180080101017. [DOI] [PubMed] [Google Scholar]
  11. Rösch J., Dotter C. T. Extrahepatic portal obstruction in childhood and its angiographic diagnosis. Am J Roentgenol Radium Ther Nucl Med. 1971 May;112(1):143–149. doi: 10.2214/ajr.112.1.143. [DOI] [PubMed] [Google Scholar]
  12. Voorhees A. B., Jr, Price J. B., Jr Extrahepatic portal hypertension. A retrospective analysis of 127 cases and associated clinical implications. Arch Surg. 1974 Mar;108(3):338–341. doi: 10.1001/archsurg.1974.01350270068012. [DOI] [PubMed] [Google Scholar]

Articles from Archives of Disease in Childhood are provided here courtesy of BMJ Publishing Group

RESOURCES