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. 1973 Mar 31;1(5856):771–773. doi: 10.1136/bmj.1.5856.771

Familial Occurrence of Persistent Müllerian Structures in Otherwise Normal Males

C G D Brook, H Wagner, M Zachmann, A Prader, S Armendares, S Frenk, P Aleman, S S Najjar, M S Slim, N Genton, C Bozic
PMCID: PMC1588901  PMID: 4144375

Abstract

Eight cases of males with persistent Müllerian structures are reported in four pairs of unrelated siblings. A genetically inherited failure to produce or to respond to the Müllerian-inhibiting substance elaborated by the fetal testis is postulated.

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Selected References

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