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. 1981 Jul;56(7):563–565. doi: 10.1136/adc.56.7.563

Purine nucleoside phosphorylase deficiency associated with a fatal lymphoproliferative disorder.

A R Watson, D I Evans, H B Marsden, V Miller, P A Rogers
PMCID: PMC1627362  PMID: 6791594

Abstract

A 2 1/2-year-old boy presented with an illness resembling glandular fever. He was found to have T-cell deficiency with lack of red and white cell purine nucleoside phosphorylase enzyme activity. A spastic tetraparesis was noted. The patient subsequently died of a malignant lymphoma of the B-immunoblastic type.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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