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. 1997 Jun;76(6):532–534. doi: 10.1136/adc.76.6.532

Severe malabsorption in autoimmune polyendocrinopathy-candidosis-ectodermal dystrophy syndrome successfully treated with immunosuppression

S Padeh 1, R Theodor 1, A Jonas 1, J Passwell 1
PMCID: PMC1717224  PMID: 9245854

Abstract

Accepted 2 January 1997


A 15 year old boy with autoimmune polyendocrinopathy-candidosis-ectodermal dystrophy syndrome suffered recurrent episodes of severe intractable diarrhoea, steatorrhoea, and hypocalcaemia. The only treatment modality, which controlled the malabsorption syndrome, was immunosuppression with intravenous high dose methylprednisolone and oral methotrexate maintenance therapy.



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Selected References

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