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. 2003 Feb;88(2):143–146. doi: 10.1136/adc.88.2.143

Partial splenectomy in cystic fibrosis patients with hypersplenism

G Thalhammer 1, E Eber 1, S Uranus 1, J Pfeifer 1, M Zach 1, D Kelly 1, de Goyet J de Ville 1
PMCID: PMC1719430  PMID: 12538318

Abstract

We report three cystic fibrosis (CF) patients with hypersplenism who underwent partial splenectomy. The postoperative course was uneventful in two patients; one patient developed a complication necessitating resection of the rest of the spleen. Haematological parameters improved and oesophageal varices regressed in all patients. On follow up, one patient showed a normal spleen, the other a normally functioning accessory spleen; the third patient again developed splenomegaly with hypersplenism. Partial splenectomy is a promising therapeutic option for CF patients with hypersplenism.

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Selected References

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