Abstract
Renal involvement has rarely been reported in patients with cystic fibrosis. We describe severe nephropathy with a rapidly fatal outcome in three adolescents with cystic fibrosis, and evaluate the important repercussions that the nephrotic syndrome had on the precarious clinical situation of these patients.
Full text
PDF
Selected References
These references are in PubMed. This may not be the complete list of references from this article.
- Abramowsky C. R., Swinehart G. L. The nephropathy of cystic fibrosis: a human model of chronic nephrotoxicity. Hum Pathol. 1982 Oct;13(10):934–939. doi: 10.1016/s0046-8177(82)80056-7. [DOI] [PubMed] [Google Scholar]
- Canciani M., Pederzini F., Mastella G., Boccato P. Systemic amyloidosis in cystic fibrosis. Acta Paediatr Scand. 1985 Jul;74(4):613–614. doi: 10.1111/j.1651-2227.1985.tb11043.x. [DOI] [PubMed] [Google Scholar]
- Coppo R., Basolo B., Martina G., Rollino C., De Marchi M., Giacchino F., Mazzucco G., Messina M., Piccoli G. Circulating immune complexes containing IgA, IgG and IgM in patients with primary IgA nephropathy and with Henoch-Schoenlein nephritis. Correlation with clinical and histologic signs of activity. Clin Nephrol. 1982 Nov;18(5):230–239. [PubMed] [Google Scholar]
- Katz S. M., Krueger L. J., Falkner B. Microscopic nephrocalcinosis in cystic fibrosis. N Engl J Med. 1988 Aug 4;319(5):263–266. doi: 10.1056/NEJM198808043190502. [DOI] [PubMed] [Google Scholar]
- Rifai A., Millard K. Glomerular deposition of immune complexes prepared with monomeric or polymeric IgA. Clin Exp Immunol. 1985 May;60(2):363–368. [PMC free article] [PubMed] [Google Scholar]
- Ristow S. C., Condemi J. J., Stuard I. D., Schwartz R. H., Bryson M. F. Systemic amyloidosis in cystic fibrosis. Am J Dis Child. 1977 Aug;131(8):886–888. doi: 10.1001/archpedi.1977.02120210064013. [DOI] [PubMed] [Google Scholar]