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. 1980 Dec;101(3):657–674.

The pathology of the feline model of mucopolysaccharidosis VI.

M E Haskins, G D Aguirre, P F Jezyk, D F Patterson
PMCID: PMC1903664  PMID: 6778219

Abstract

Three cats with feline arylsulfatase-B--deficient mucopolysaccharidosis were studied by light and transmission electron microscopy. Membrane-bound cytoplasmic inclusions were present in hepatocytes, bone marrow granulocytes, vascular smooth muscle cells, and fibroblasts in skin, cornea, and cardiac valves. Central nervous system lesions were restricted to mild ventricular dilatation, perithelial cell vacuolation, and, in one animal, cord compression by vertebral exostoses. The lesions in these cats closely resembled those described in human patients with mucopolysaccharidosis VI (Maroteaux-Lamy syndrome).

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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