Abstract
An unusual association of malformations of the right lung was observed in two patients, and 36 similar cases were briefly reviewed. Findings included: (1) anomalous return of the right pulmonary veins, via a common channel, to the inferior vena cava, giving a typical radiological picture; (2) hypoplasia or absence of two major bronchi on the right side; (3) absence of the right pulmonary artery in one patient and hypoplasia in the other; (4) secondary dextroposition of the heart; (5) presence of a left-to-right shunt, through this abnormal circulation, varying from very small in one patient to more than 30% of the pulmonary blood flow in the other. When found together, these anomalies constitute a specific entity, the scimitar syndrome.
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