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- BRENTON D. P., CUSWORTH D. C., GAULL G. E. HOMOCYSTINURIA. BIOCHEMICAL STUDIES OF TISSUES INCLUDING A COMPARISON WITH CYSTATHIONINURIA. Pediatrics. 1965 Jan;35:50–56. [PubMed] [Google Scholar]
- CAVALLINI D., MONDOVI B., DE MARCO C., SCIOSCIA-SANTORO A. The mechanism of desulphhydration of cysteine. Enzymologia. 1962 Jun 30;24:253–266. [PubMed] [Google Scholar]
- CHATAGNER F. OCCURRENCE OF HOMOSERINE IN THE LIVER OF ETHIONINE- OR METHIONINE-TREATED RATS. Nature. 1964 Sep 12;203:1177–1178. doi: 10.1038/2031177b0. [DOI] [PubMed] [Google Scholar]
- EFRON M. L. AMINOACIDURIA. N Engl J Med. 1965 May 27;272:1107–CONCL. doi: 10.1056/NEJM196505272722107. [DOI] [PubMed] [Google Scholar]
- FERNANDEZ J., HORVATH A. THE ROLE OF THYROID HORMONES IN TRANSSULPHURATION. I. INHIBITION OF CYSTATHIONASE BY THYROXINE. Enzymologia. 1963 Sep 30;26:113–124. [PubMed] [Google Scholar]
- FINKELSTEIN J. D., MUDD S. H., IRREVERRE F., LASTER L. HOMOCYSTINURIA DUE TO CYSTATHIONINE SYNTHETASE DEFICIENCY: THE MODE OF INHERITANCE. Science. 1964 Nov 6;146(3645):785–787. doi: 10.1126/science.146.3645.785. [DOI] [PubMed] [Google Scholar]
- FLAVIN M., SLAUGHTER C. AN INTERMEDIATE TRAPPED BY MALEIMIDES IN A PYRIDOXAL-PHOSPHATE POTENTIATED ENZYMATIC ELIMINATION REACTION. Biochemistry. 1964 Jul;3:885–893. doi: 10.1021/bi00895a004. [DOI] [PubMed] [Google Scholar]
- FRIMPTER G. W., HAYMOVITZ A., HORWITH M. Cystathioninura. N Engl J Med. 1963 Feb 14;268:333–339. doi: 10.1056/NEJM196302142680701. [DOI] [PubMed] [Google Scholar]
- Frimpter G. W. Cystathioninuria: nature of the defect. Science. 1965 Sep 3;149(3688):1095–1096. doi: 10.1126/science.149.3688.1095. [DOI] [PubMed] [Google Scholar]
- GREENBERG D. M., MATSUO Y., ROTHSTEIN M. Metabolic pathways of homoserine in the mammal. J Biol Chem. 1956 Aug;221(2):679–687. [PubMed] [Google Scholar]
- HARRIS H., PENROSE L. S., THOMAS D. H. Cystathioniuria. Ann Hum Genet. 1959 Dec;23:442–453. doi: 10.1111/j.1469-1809.1959.tb01485.x. [DOI] [PubMed] [Google Scholar]
- HOPE D. B. L-cystathionine in the urine of pyridoxine-deficient rats. Biochem J. 1957 Jul;66(3):486–489. doi: 10.1042/bj0660486. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Homocystinuria due to cystathionine synthase deficiency. Ann Intern Med. 1965 Dec;63(6):1117–1142. doi: 10.7326/0003-4819-63-6-1117. [DOI] [PubMed] [Google Scholar]
- JOLLES BERGERET B., CHATAGNER F. EFFECT OF 2-MERCAPTOETHANOL ON THE DEAMINATION OF L-CYSTEINE BY CYSTATHIONASE OF RAT LIVER. Arch Biochem Biophys. 1964 Jun;105:640–641. doi: 10.1016/0003-9861(64)90062-1. [DOI] [PubMed] [Google Scholar]
- JOLLES-BERGERET B., LABOUESSE J., CHATAGNER F. [Influence of thyroid hormones on the desulfuration of cysteine by rat liver. Comparison of the behavior of the desulfuration with that of other enzymatic reactions requiring pyridoxal phosphate]. Bull Soc Chim Biol (Paris) 1960;42:51–63. [PubMed] [Google Scholar]
- LOISELET J., CHATAGNER F. LA L-CYST'EINE EST-ELLE VRAIMENT SUBSTRAT DE LA CYSTATHIONASE? Biochim Biophys Acta. 1964 Aug 26;89:330–336. [PubMed] [Google Scholar]
- Laster L., Mudd S. H., Finkelstein J. D., Irreverre F. Homocystinuria due to cystathionine synthase deficiency: the metabolism of L-methionine. J Clin Invest. 1965 Oct;44(10):1708–1719. doi: 10.1172/JCI105278. [DOI] [PMC free article] [PubMed] [Google Scholar]
- MATSUO Y., GREENBERG D. M. A crystalline enzyme that cleaves homoserine and cystathionine. I. Isolation procedure and some physicochemical properties. J Biol Chem. 1958 Feb;230(2):545–560. [PubMed] [Google Scholar]
- MATSUO Y., GREENBERG D. M. A crystalline enzyme that cleaves homoserine and cystathionine. II. Prosthetic group. J Biol Chem. 1958 Feb;230(2):561–571. [PubMed] [Google Scholar]
- MATSUO Y., GREENBERG D. M. A crystalline enzyme that cleaves homoserine and cystathionine. IV. Mechanism of action, reversibility, and substrate specificity. J Biol Chem. 1959 Mar;234(3):516–519. [PubMed] [Google Scholar]
- MATSUO Y., GREENBERG D. M. Metabolic formation of homoserine and alpha-aminobutyric acid from methionine. J Biol Chem. 1955 Aug;215(2):547–554. [PubMed] [Google Scholar]
- MUDD S. H., FINKELSTEIN J. D., IRREVERRE F., LASTER L. HOMOCYSTINURIA: AN ENZYMATIC DEFECT. Science. 1964 Mar 27;143(3613):1443–1445. doi: 10.1126/science.143.3613.1443. [DOI] [PubMed] [Google Scholar]
- Mudd S. H., Finkelstein J. D., Irreverre F., Laster L. Threonine dehydratase activity in humans lacking cystathionine synthase. Biochem Biophys Res Commun. 1965 May 18;19(5):665–670. doi: 10.1016/0006-291x(65)90392-x. [DOI] [PubMed] [Google Scholar]
- Mudd S. H., Finkelstein J. D., Irreverre F., Laster L. Transsulfuration in mammals. Microassays and tissue distributions of three enzymes of the pathway. J Biol Chem. 1965 Nov;240(11):4382–4392. [PubMed] [Google Scholar]
- TRAUTMANN O., CHATAGNER F. ADAPTATION M'ETABOLIQUE DE LA CYSTATHIONASE DU FOIE DE RAT. Bull Soc Chim Biol (Paris) 1964;46:129–139. [PubMed] [Google Scholar]