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. 1988;99:57–67.

Lymphangiomyomatosis: a respiratory illness with an endocrinologic therapy.

H O Sieker 1, K S McCarty Jr 1
PMCID: PMC2376424  PMID: 3503438

Abstract

Lymphangiomyomatosis should be considered when unexplained dyspnea, pneumothorax, pleural effusion or infiltrative radiographic changes occurs in a woman of childbearing age. Radiographic and pulmonary function peculiarities help in the diagnosis and evaluation of results of treatment. Diagnosis is dependent on lung biopsy and preferably identification of hormonal receptors. Endocrinological manipulation, in this study with medroxyprogesterone, decreased disability, morbidity and progression of this otherwise fatal illness. Early diagnosis and institution of treatment would appear to provide the best result.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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