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. 2004 Mar;8(1):51–56. doi: 10.1080/13577140410001679275

Giant Osteofibrous Dysplasia (Ossifying Fibroma) of the Tibia: Case Report and Review of Treatment Modalities

Eitan Segev 1,✉, Josephine Issakov 3, Eli Ezra 1, Shlomo Wientroub 1, Itzchak Meller 2
PMCID: PMC2395597  PMID: 18521395

Abstract

We present a case of giant osteofibrous dysplasia (OFB) of the proximal tibia with 15 years of follow-up. The tumor recurred after first biopsy and curettage done at the age of 6 years and, again, 4 years later. Following recurrence, the option of amputation was suggested. Staged treatment of curettage, cryosurgery, bone cement as a temporary spacer with internal fixation at age 12 years, followed by bone grafting at age 14 years, led to complete healing. The staged protocol for treatment is proposed as an alternative to more radical solutions. It is suggested to postpone surgical treatment towards skeletal maturity.

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Selected References

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