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Selected References
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- Ball R., Chetcuti P. A., Beverley D. Fatal familial surfactant protein B deficiency. Arch Dis Child Fetal Neonatal Ed. 1995 Jul;73(1):F53–F53. doi: 10.1136/fn.73.1.f53. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Cochrane C. G., Revak S. D. Pulmonary surfactant protein B (SP-B): structure-function relationships. Science. 1991 Oct 25;254(5031):566–568. doi: 10.1126/science.1948032. [DOI] [PubMed] [Google Scholar]
- Coleman M., Dehner L. P., Sibley R. K., Burke B. A., L'Heureux P. R., Thompson T. R. Pulmonary alveolar proteinosis: an uncommon cause of chronic neonatal respiratory distress. Am Rev Respir Dis. 1980 Mar;121(3):583–586. doi: 10.1164/arrd.1980.121.3.583. [DOI] [PubMed] [Google Scholar]
- Hamvas A., Cole F. S., deMello D. E., Moxley M., Whitsett J. A., Colten H. R., Nogee L. M. Surfactant protein B deficiency: antenatal diagnosis and prospective treatment with surfactant replacement. J Pediatr. 1994 Sep;125(3):356–361. doi: 10.1016/s0022-3476(05)83276-7. [DOI] [PubMed] [Google Scholar]
- Hamvas A., Nogee L. M., deMello D. E., Cole F. S. Pathophysiology and treatment of surfactant protein-B deficiency. Biol Neonate. 1995;67 (Suppl 1):18–31. doi: 10.1159/000244204. [DOI] [PubMed] [Google Scholar]
- Hawgood S., Latham D., Borchelt J., Damm D., White T., Benson B., Wright J. R. Cell-specific posttranslational processing of the surfactant-associated protein SP-B. Am J Physiol. 1993 Mar;264(3 Pt 1):L290–L299. doi: 10.1152/ajplung.1993.264.3.L290. [DOI] [PubMed] [Google Scholar]
- Herman T. E., Nogee L. M., McAlister W. H., Dehner L. P. Surfactant protein B deficiency: radiographic manifestations. Pediatr Radiol. 1993;23(5):373–375. doi: 10.1007/BF02011963. [DOI] [PubMed] [Google Scholar]
- Knight D. P., Knight J. A. Pulmonary alveolar proteinosis in the newborn. Arch Pathol Lab Med. 1985 Jun;109(6):529–531. [PubMed] [Google Scholar]
- Longo M. L., Bisagno A. M., Zasadzinski J. A., Bruni R., Waring A. J. A function of lung surfactant protein SP-B. Science. 1993 Jul 23;261(5120):453–456. doi: 10.1126/science.8332910. [DOI] [PubMed] [Google Scholar]
- Moulton S. L., Krous H. F., Merritt T. A., Odell R. M., Gangitano E., Cornish J. D. Congenital pulmonary alveolar proteinosis: failure of treatment with extracorporeal life support. J Pediatr. 1992 Feb;120(2 Pt 1):297–302. doi: 10.1016/s0022-3476(05)80448-2. [DOI] [PubMed] [Google Scholar]
- Nogee L. M., Garnier G., Dietz H. C., Singer L., Murphy A. M., deMello D. E., Colten H. R. A mutation in the surfactant protein B gene responsible for fatal neonatal respiratory disease in multiple kindreds. J Clin Invest. 1994 Apr;93(4):1860–1863. doi: 10.1172/JCI117173. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Nogee L. M., de Mello D. E., Dehner L. P., Colten H. R. Brief report: deficiency of pulmonary surfactant protein B in congenital alveolar proteinosis. N Engl J Med. 1993 Feb 11;328(6):406–410. doi: 10.1056/NEJM199302113280606. [DOI] [PubMed] [Google Scholar]
- Pilot-Matias T. J., Kister S. E., Fox J. L., Kropp K., Glasser S. W., Whitsett J. A. Structure and organization of the gene encoding human pulmonary surfactant proteolipid SP-B. DNA. 1989 Mar;8(2):75–86. doi: 10.1089/dna.1.1989.8.75. [DOI] [PubMed] [Google Scholar]
- Possmayer F. A proposed nomenclature for pulmonary surfactant-associated proteins. Am Rev Respir Dis. 1988 Oct;138(4):990–998. doi: 10.1164/ajrccm/138.4.990. [DOI] [PubMed] [Google Scholar]
- Pryhuber G. S., Hull W. M., Fink I., McMahan M. J., Whitsett J. A. Ontogeny of surfactant proteins A and B in human amniotic fluid as indices of fetal lung maturity. Pediatr Res. 1991 Dec;30(6):597–605. doi: 10.1203/00006450-199112000-00023. [DOI] [PubMed] [Google Scholar]
- Robertson B., Kobayashi T., Ganzuka M., Grossmann G., Li W. Z., Suzuki Y. Experimental neonatal respiratory failure induced by a monoclonal antibody to the hydrophobic surfactant-associated protein SP-B. Pediatr Res. 1991 Sep;30(3):239–243. doi: 10.1203/00006450-199109000-00007. [DOI] [PubMed] [Google Scholar]
- Rogers B. B., Alpert L. C., Hine E. A., Buffone G. J. Analysis of DNA in fresh and fixed tissue by the polymerase chain reaction. Am J Pathol. 1990 Mar;136(3):541–548. [PMC free article] [PubMed] [Google Scholar]
- Schumacher R. E., Marrogi A. J., Heidelberger K. P. Pulmonary alveolar proteinosis in a newborn. Pediatr Pulmonol. 1989;7(3):178–182. doi: 10.1002/ppul.1950070312. [DOI] [PubMed] [Google Scholar]
- Schägger H., von Jagow G. Tricine-sodium dodecyl sulfate-polyacrylamide gel electrophoresis for the separation of proteins in the range from 1 to 100 kDa. Anal Biochem. 1987 Nov 1;166(2):368–379. doi: 10.1016/0003-2697(87)90587-2. [DOI] [PubMed] [Google Scholar]
- Suzuki Y., Fujita Y., Kogishi K. Reconstitution of tubular myelin from synthetic lipids and proteins associated with pig pulmonary surfactant. Am Rev Respir Dis. 1989 Jul;140(1):75–81. doi: 10.1164/ajrccm/140.1.75. [DOI] [PubMed] [Google Scholar]
- Teja K., Cooper P. H., Squires J. E., Schnatterly P. T. Pulmonary alveolar proteinosis in four siblings. N Engl J Med. 1981 Dec 3;305(23):1390–1392. doi: 10.1056/NEJM198112033052305. [DOI] [PubMed] [Google Scholar]
- Venkatesh V. C., Iannuzzi D. M., Ertsey R., Ballard P. L. Differential glucocorticoid regulation of the pulmonary hydrophobic surfactant proteins SP-B and SP-C. Am J Respir Cell Mol Biol. 1993 Feb;8(2):222–228. doi: 10.1165/ajrcmb/8.2.222. [DOI] [PubMed] [Google Scholar]
- Weaver T. E., Whitsett J. A. Function and regulation of expression of pulmonary surfactant-associated proteins. Biochem J. 1991 Jan 15;273(Pt 2):249–264. doi: 10.1042/bj2730249. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Yei S., Bachurski C. J., Weaver T. E., Wert S. E., Trapnell B. C., Whitsett J. A. Adenoviral-mediated gene transfer of human surfactant protein B to respiratory epithelial cells. Am J Respir Cell Mol Biol. 1994 Sep;11(3):329–336. doi: 10.1165/ajrcmb.11.3.8086169. [DOI] [PubMed] [Google Scholar]
- deMello D. E., Nogee L. M., Heyman S., Krous H. F., Hussain M., Merritt T. A., Hsueh W., Haas J. E., Heidelberger K., Schumacher R. Molecular and phenotypic variability in the congenital alveolar proteinosis syndrome associated with inherited surfactant protein B deficiency. J Pediatr. 1994 Jul;125(1):43–50. doi: 10.1016/s0022-3476(94)70119-9. [DOI] [PubMed] [Google Scholar]
- deMello D. E., Phelps D. S., Patel G., Floros J., Lagunoff D. Expression of the 35kDa and low molecular weight surfactant-associated proteins in the lungs of infants dying with respiratory distress syndrome. Am J Pathol. 1989 Jun;134(6):1285–1293. [PMC free article] [PubMed] [Google Scholar]
- van Golde L. M. Potential role of surfactant proteins A and D in innate lung defense against pathogens. Biol Neonate. 1995;67 (Suppl 1):2–17. doi: 10.1159/000244202. [DOI] [PubMed] [Google Scholar]
