Skip to main content
The Journal of Clinical Investigation logoLink to The Journal of Clinical Investigation
. 1966 Jun;45(6):880–890. doi: 10.1172/JCI105403

Hereditary deficiency of the second component of complement (C'2) in man.

M R Klemperer, H C Woodworth, F S Rosen, K F Austen
PMCID: PMC292767  PMID: 4161820

Full text

PDF
880

Images in this article

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. AUSTEN K. F., BEER F. THE MEASUREMENT OF SECOND COMPONENT OF HUMAN COMPLEMENT (C'2HU) BY ITS INTERACTION WITH EAC'1AGP,4GP CELLS. J Immunol. 1964 Jun;92:946–957. [PubMed] [Google Scholar]
  2. AUSTEN K. F., SHEFFER A. L. DETECTION OF HEREDITARY ANGIONEUROTIC EDEMA BY DEMONSTRATION OF A REDUCTION IN THE SECOND COMPONENT OF HUMAN COMPLEMENT. N Engl J Med. 1965 Apr 1;272:649–656. doi: 10.1056/NEJM196504012721301. [DOI] [PubMed] [Google Scholar]
  3. CINADER B., DUBISKI S., WARDLAW A. C. DISTRIBUTION, INHERITANCE, AND PROPERTIES OF AN ANTIGEN, MUB1, AND ITS RELATION TO HEMOLYTIC COMPLEMENT. J Exp Med. 1964 Nov 1;120:897–924. doi: 10.1084/jem.120.5.897. [DOI] [PMC free article] [PubMed] [Google Scholar]
  4. DONALDSON V. H., ROSEN F. S. ACTION OF COMPLEMENT IN HEREDITARY ANGIONEUROTIC EDEMA: THE ROLE OF C'1-ESTERASE. J Clin Invest. 1964 Nov;43:2204–2213. doi: 10.1172/JCI105094. [DOI] [PMC free article] [PubMed] [Google Scholar]
  5. FISCHEL E. E., GAJDUSEK D. C. Serum complement in acute glomerulonephritis and other renal diseases. Am J Med. 1952 Feb;12(2):190–196. doi: 10.1016/0002-9343(52)90211-8. [DOI] [PubMed] [Google Scholar]
  6. GREEN H., FLEISCHER R. A., BARROW P., GOLDBERG B. The cytotoxic action of immune gamma globulin and complement on Krebs ascites tumor cells. II. Chemical studies. J Exp Med. 1959 May 1;109(5):511–521. doi: 10.1084/jem.109.5.511. [DOI] [PMC free article] [PubMed] [Google Scholar]
  7. HERZENBERG L. A., TACHIBANA D. K., HERZENBERG L. A., ROSENBERG L. T. A gene locus concerned with hemolytic complement in Mus musculus. Genetics. 1963 May;48:711–715. doi: 10.1093/genetics/48.5.711. [DOI] [PMC free article] [PubMed] [Google Scholar]
  8. KLEMPERER M. R., GOTOFF S. P., ALPER C. A., LEVIN A. S., ROSEN F. S. ESTIMATION OF THE SERUM BETA-1C GLOBULIN CONCENTRATION: ITS RELATION TO THE SERUM HEMOLYTIC COMPLEMENT TITER. Pediatrics. 1965 May;35:765–769. [PubMed] [Google Scholar]
  9. LANGE K., GRAIG F., OBERMAN J., SLOBODY L., OGUR G., LoCASTO F. Changes in serum complement during the course and treatment of glomerulonephritis. AMA Arch Intern Med. 1951 Oct;88(4):433–445. doi: 10.1001/archinte.1951.03810100017002. [DOI] [PubMed] [Google Scholar]
  10. LANGE K., WASSERMAN E., SLOBODY L. B. The significance of serum complement levels for the diagnosis and prognosis of acute and subacute glomerulonephritis and lupus erythematosus disseminatus. Ann Intern Med. 1960 Oct;53:636–646. doi: 10.7326/0003-4819-53-4-636. [DOI] [PubMed] [Google Scholar]
  11. LEVY L. R., LEPOW I. H. Assay and properties of serum inhibitor of C'l-esterase. Proc Soc Exp Biol Med. 1959 Aug-Sep;101:608–611. doi: 10.3181/00379727-101-25034. [DOI] [PubMed] [Google Scholar]
  12. MAYER M. M. On the destruction of erythrocytes and other cells by antibody and complement. Cancer Res. 1961 Oct;21:1262–1269. [PubMed] [Google Scholar]
  13. MICHAEL J. G., WHITBY J. L., LANDY M. Studies on natural antibodies to gram-negative bacteria. J Exp Med. 1962 Jan 1;115:131–146. doi: 10.1084/jem.115.1.131. [DOI] [PMC free article] [PubMed] [Google Scholar]
  14. MULLER-EBERHARD H. J., NILSSON U., ARONSSON T. Isolation and characterization of two beta1-glycoproteins of human serum. J Exp Med. 1960 Feb 1;111:201–215. doi: 10.1084/jem.111.2.201. [DOI] [PMC free article] [PubMed] [Google Scholar]
  15. MUSCHEL L. H., TREFFERS H. P. Quantitative studies on the bactericidal actions of serum and complement. II. Some implications for the mechanism of the bactericidal reaction. J Immunol. 1956 Jan;76(1):11–19. [PubMed] [Google Scholar]
  16. NISHIOKA K. Measurements of complement by agglutination of human erythrocytes reacting in immune-adherence. J Immunol. 1963 Jan;90:86–97. [PubMed] [Google Scholar]
  17. ROSENBERG L. T., TACHIBANA D. K. Activity of mouse complement. J Immunol. 1962 Dec;89:861–867. [PubMed] [Google Scholar]
  18. ROSEN F. S., PENSKY J., DONALDSON V., CHARACHE P. HEREDITARY ANGIONEUROTIC EDEMA: TWO GENETIC VARIANTS. Science. 1965 May 14;148(3672):957–958. doi: 10.1126/science.148.3672.957. [DOI] [PubMed] [Google Scholar]
  19. ROSS A., LEPOW I. H. Studies on immune cellular injury. I. Cytotoxic effects of antibody and complement. J Exp Med. 1960 Dec 1;112:1085–1106. doi: 10.1084/jem.112.6.1085. [DOI] [PMC free article] [PubMed] [Google Scholar]
  20. ROTHER K., ROTHER U., PETERSEN K. F., GEMSA D., MITZE F. IMMUNE BACTERICIDAL ACTIVITY OF COMPLEMENT. SEPARATION AND DESCRIPTION OF INTERMEDIATE STEPS. J Immunol. 1964 Aug;93:319–330. [PubMed] [Google Scholar]
  21. Rother K., Rother U. Studies on complement defective rabbits. IV. Blood clearance of intravenously injected S. typhi by the reticuloendothelial system. Proc Soc Exp Biol Med. 1965 Aug-Sep;119(4):1055–1059. doi: 10.3181/00379727-119-30375. [DOI] [PubMed] [Google Scholar]
  22. SCHEIDEGGER J. J. Une micro-méthode de l'immuno-electrophorèse. Int Arch Allergy Appl Immunol. 1955;7(2):103–110. [PubMed] [Google Scholar]
  23. SILVERSTEIN A. M. Essential hypocomplementemia: report of a case. Blood. 1960 Sep;16:1338–1341. [PubMed] [Google Scholar]
  24. STIFFEL C., BIOZZI G., MOUTON D., BOUTHILLIER Y., DECREUSEFOND C. STUDIES ON PHAGOCYTOSIS OF BACTERIA BY THE RETICULOENDOTHELIAL SYSTEM IN A STRAIN OF MICE LACKING HEMOLYTIC COMPLEMENT. J Immunol. 1964 Aug;93:246–249. [PubMed] [Google Scholar]
  25. Suskind S. R., Yanofsky C., Bonner D. M. ALLELIC STRAINS OF Neurospora LACKING TRYPTOPHAN SYNTHETASE: A PRELIMINARY IMMUNOCHEMICAL CHARACTERIZATION. Proc Natl Acad Sci U S A. 1955 Aug 15;41(8):577–582. doi: 10.1073/pnas.41.8.577. [DOI] [PMC free article] [PubMed] [Google Scholar]
  26. WARD P. A., COCHRANE C. G., MUELLER-EBERHARD H. J. THE ROLE OF SERUM COMPLEMENT IN CHEMOTAXIS OF LEUKOCYTES IN VITRO. J Exp Med. 1965 Aug 1;122:327–346. doi: 10.1084/jem.122.2.327. [DOI] [PMC free article] [PubMed] [Google Scholar]
  27. WEDGWOOD R. J. P., JANEWAY C. A. Serum complement in children with collagen diseases. Pediatrics. 1953 Jun;11(6):569–581. [PubMed] [Google Scholar]
  28. WEDGWOOD R. J. Measurement of the components of complement by the reagent titration technique. Z Immun exp ther. 1959 Oct-Nov;118:358–367. [PubMed] [Google Scholar]
  29. WOODWORTH H. C. Studies with immune-adherence. I. Titration of human complement with a rice starch system. Immunology. 1962 Jan;5:181–186. [PMC free article] [PubMed] [Google Scholar]

Articles from Journal of Clinical Investigation are provided here courtesy of American Society for Clinical Investigation

RESOURCES