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. 1997;24(4):301–307.

Congenital complete atrioventricular block.

N J Kertesz 1, A L Fenrich 1, R A Friedman 1
PMCID: PMC325472  PMID: 9456483

Abstract

Congenital complete atrioventricular block is found in 1 of 22,000 live births. Over time, it has become apparent that these patients represent not a single distinct disease process, but several processes with the common manifestation of atrioventricular block. The evaluation of these patients to determine their risk of sudden death and need for pacing is not well defined.

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Selected References

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  1. Anderson R. H., Wenick A. C., Losekoot T. G., Becker A. E. Congenitally complete heart block. Developmental aspects. Circulation. 1977 Jul;56(1):90–101. doi: 10.1161/01.cir.56.1.90. [DOI] [PubMed] [Google Scholar]
  2. Benson D. W., Jr, Spach M. S., Edwards S. B., Sterba R., Serwer G. A., Armstrong B. E., Anderson P. A. Heart block in children. Evaluation of subsidiary ventricular pacemaker recovery times and ECG tape recordings. Pediatr Cardiol. 1982;2(1):39–45. doi: 10.1007/BF02265615. [DOI] [PubMed] [Google Scholar]
  3. Camm A. J., Bexton R. S. Congenital complete heart block. Eur Heart J. 1984 Mar;5 (Suppl A):115–117. doi: 10.1093/eurheartj/5.suppl_a.115. [DOI] [PubMed] [Google Scholar]
  4. Campbell M., Emanuel R. Six cases of congenital complete heart block followed for 34-40 years. Br Heart J. 1967 Jul;29(4):577–587. doi: 10.1136/hrt.29.4.577. [DOI] [PMC free article] [PubMed] [Google Scholar]
  5. Cecconi M., Renzi R., Bettuzzi M. G., Colonna P., Cuccaroni G., Ricciotti R., Pozzato E., Berrettini U., Sgarbi E., Sparvieri F. Blocco atrioventricolare completo congenito isolato: esperienza a lungo termine in 38 pazienti. G Ital Cardiol. 1993 Jan;23(1):39–53. [PubMed] [Google Scholar]
  6. Chameides L., Truex R. C., Vetter V., Rashkind W. J., Galioto F. M., Jr, Noonan J. A. Association of maternal systemic lupus erythematosus with congenital complete heart block. N Engl J Med. 1977 Dec 1;297(22):1204–1207. doi: 10.1056/NEJM197712012972203. [DOI] [PubMed] [Google Scholar]
  7. Corne R. A., Mathewson F. A. Congenital complete atrioventricular heart block. A 25 year follow-up study. Am J Cardiol. 1972 Mar;29(3):412–415. doi: 10.1016/0002-9149(72)90540-1. [DOI] [PubMed] [Google Scholar]
  8. Crawford D., Chapman M., Allan L. The assessment of persistent bradycardia in prenatal life. Br J Obstet Gynaecol. 1985 Sep;92(9):941–944. doi: 10.1111/j.1471-0528.1985.tb03074.x. [DOI] [PubMed] [Google Scholar]
  9. Daliento L., Corrado D., Buja G., John N., Nava A., Thiene G. Rhythm and conduction disturbances in isolated, congenitally corrected transposition of the great arteries. Am J Cardiol. 1986 Aug 1;58(3):314–318. doi: 10.1016/0002-9149(86)90069-x. [DOI] [PubMed] [Google Scholar]
  10. Derksen R. H., Meilof J. F. Anti-Ro/SS-A and anti-La/SS-B autoantibody levels in relation to systemic lupus erythematosus disease activity and congenital heart block. A longitudinal study comprising two consecutive pregnancies in a patient with systemic lupus erythematosus. Arthritis Rheum. 1992 Aug;35(8):953–959. doi: 10.1002/art.1780350817. [DOI] [PubMed] [Google Scholar]
  11. Dewey R. C., Capeless M. A., Levy A. M. Use of ambulatory electrocardiographic monitoring to identify high-risk patients with congenital complete heart block. N Engl J Med. 1987 Apr 2;316(14):835–839. doi: 10.1056/NEJM198704023161403. [DOI] [PubMed] [Google Scholar]
  12. Dreifus L. S., Fisch C., Griffin J. C., Gillette P. C., Mason J. W., Parsonnet V. Guidelines for implantation of cardiac pacemakers and antiarrhythmia devices. A report of the American College of Cardiology/American Heart Association Task Force on Assessment of Diagnostic and Therapeutic Cardiovascular Procedures. (Committee on Pacemaker Implantation). Circulation. 1991 Jul;84(1):455–467. doi: 10.1161/01.cir.84.1.455. [DOI] [PubMed] [Google Scholar]
  13. Dörner T., Hiepe F., Göldner B., Apostoloff E. Investigations into Ro-specific antibody-associated congenital cardiac conduction defects. Clin Investig. 1992 Jun;70(6):492–496. doi: 10.1007/BF00210230. [DOI] [PubMed] [Google Scholar]
  14. Esscher E., Michaëlsson M. Q-T interval in congenital complete heart block. Pediatr Cardiol. 1983 Apr-Jun;4(2):121–124. doi: 10.1007/BF02076336. [DOI] [PubMed] [Google Scholar]
  15. Ferguson J. J. American College of Cardiology 45th Annual Scientific Session, Orlando, Florida, March 24 to 27, 1996. Circulation. 1996 Jul 1;94(1):1–5. doi: 10.1161/01.cir.94.1.1. [DOI] [PubMed] [Google Scholar]
  16. GOCHBERG S. H. CONGENITAL HEART BLOCK. Am J Obstet Gynecol. 1964 Jan 15;88:238–241. doi: 10.1016/0002-9378(64)90262-5. [DOI] [PubMed] [Google Scholar]
  17. Huhta J. C., Maloney J. D., Ritter D. G., Ilstrup D. M., Feldt R. H. Complete atrioventricular block in patients with atrioventricular discordance. Circulation. 1983 Jun;67(6):1374–1377. doi: 10.1161/01.cir.67.6.1374. [DOI] [PubMed] [Google Scholar]
  18. IKKOS D., HANSON J. S. Response to exercise in congenital complete atrioventricular block. Circulation. 1960 Oct;22:583–590. doi: 10.1161/01.cir.22.4.583. [DOI] [PubMed] [Google Scholar]
  19. Kaaja R., Julkunen H., Ammälä P., Kurki P., Koskimies S. Congenital heart block in one of the HLA identical twins. Eur J Obstet Gynecol Reprod Biol. 1993 Sep;51(1):78–80. doi: 10.1016/0028-2243(93)90194-h. [DOI] [PubMed] [Google Scholar]
  20. Karpawich P. P., Gillette P. C., Garson A., Jr, Hesslein P. S., Porter C. B., McNamara D. G. Congenital complete atrioventricular block: clinical and electrophysiologic predictors of need for pacemaker insertion. Am J Cardiol. 1981 Dec;48(6):1098–1102. doi: 10.1016/0002-9149(81)90326-x. [DOI] [PubMed] [Google Scholar]
  21. Kay H. B. VENTRICULAR COMPLEXES IN HEART BLOCK. Br Heart J. 1948 Jul;10(3):177–187. doi: 10.1136/hrt.10.3.177. [DOI] [PMC free article] [PubMed] [Google Scholar]
  22. Lev M. Pathogenesis of congenital atrioventricular block. Prog Cardiovasc Dis. 1972 Sep-Oct;15(2):145–157. doi: 10.1016/0033-0620(72)90016-3. [DOI] [PubMed] [Google Scholar]
  23. Levy A. M., Camm A. J., Keane J. F. Multiple arrhythmias detected during nocturnal monitoring in patients with congenital complete heart block. Circulation. 1977 Feb;55(2):247–253. doi: 10.1161/01.cir.55.2.247. [DOI] [PubMed] [Google Scholar]
  24. Litsey S. E., Noonan J. A., O'Connor W. N., Cottrill C. M., Mitchell B. Maternal connective tissue disease and congenital heart block. Demonstration of immunoglobulin in cardiac tissue. N Engl J Med. 1985 Jan 10;312(2):98–100. doi: 10.1056/NEJM198501103120206. [DOI] [PubMed] [Google Scholar]
  25. Lockshin M. D., Bonfa E., Elkon K., Druzin M. L. Neonatal lupus risk to newborns of mothers with systemic lupus erythematosus. Arthritis Rheum. 1988 Jun;31(6):697–701. doi: 10.1002/art.1780310601. [DOI] [PubMed] [Google Scholar]
  26. Lundstrom U., Bull C., Wyse R. K., Somerville J. The natural and "unnatural" history of congenitally corrected transposition. Am J Cardiol. 1990 May 15;65(18):1222–1229. doi: 10.1016/0002-9149(90)90978-a. [DOI] [PubMed] [Google Scholar]
  27. Machado M. V., Tynan M. J., Curry P. V., Allan L. D. Fetal complete heart block. Br Heart J. 1988 Dec;60(6):512–515. doi: 10.1136/hrt.60.6.512. [DOI] [PMC free article] [PubMed] [Google Scholar]
  28. Manno B. V., Hakki A. H., Eshaghpour E., Iskandrian A. S. Left ventricular function at rest and during exercise in congenital complete heart block: a radionuclide angiographic evaluation. Am J Cardiol. 1983 Jul;52(1):92–94. doi: 10.1016/0002-9149(83)90076-0. [DOI] [PubMed] [Google Scholar]
  29. McCue C. M., Mantakas M. E., Tingelstad J. B., Ruddy S. Congenital heart block in newborns of mothers with connective tissue disease. Circulation. 1977 Jul;56(1):82–90. doi: 10.1161/01.cir.56.1.82. [DOI] [PubMed] [Google Scholar]
  30. McHenry M. M. Factors influencing longevity in adults with congenital complete heart block. Am J Cardiol. 1972 Mar;29(3):416–421. doi: 10.1016/0002-9149(72)90541-3. [DOI] [PubMed] [Google Scholar]
  31. Michaëlsson M., Engle M. A. Congenital complete heart block: an international study of the natural history. Cardiovasc Clin. 1972;4(3):85–101. [PubMed] [Google Scholar]
  32. Michaëlsson M., Jonzon A., Riesenfeld T. Isolated congenital complete atrioventricular block in adult life. A prospective study. Circulation. 1995 Aug 1;92(3):442–449. doi: 10.1161/01.cir.92.3.442. [DOI] [PubMed] [Google Scholar]
  33. NAKAMURA F. F., NADAS A. S. COMPLETE HEART BLOCK IN INFANTS AND CHILDREN. N Engl J Med. 1964 Jun 11;270:1261–1268. doi: 10.1056/NEJM196406112702401. [DOI] [PubMed] [Google Scholar]
  34. Pinsky W. W., Gillette P. C., Garson A., Jr, McNamara D. G. Diagnosis, management, and long-term results of patients with congenital complete atrioventricular block. Pediatrics. 1982 Jun;69(6):728–733. [PubMed] [Google Scholar]
  35. Pordon C. M., Moodie D. S. Adults with congenital complete heart block: 25-year follow-up. Cleve Clin J Med. 1992 Nov-Dec;59(6):587–590. doi: 10.3949/ccjm.59.6.587. [DOI] [PubMed] [Google Scholar]
  36. Ramsey-Goldman R., Hom D., Deng J. S., Ziegler G. C., Kahl L. E., Steen V. D., LaPorte R. E., Medsger T. A., Jr Anti-SS-A antibodies and fetal outcome in maternal systemic lupus erythematosus. Arthritis Rheum. 1986 Oct;29(10):1269–1273. doi: 10.1002/art.1780291013. [DOI] [PubMed] [Google Scholar]
  37. Reybrouck T., Vanden Eynde B., Dumoulin M., Van der Hauwaert L. G. Cardiorespiratory response to exercise in congenital complete atrioventricular block. Am J Cardiol. 1989 Oct 15;64(14):896–899. doi: 10.1016/0002-9149(89)90838-2. [DOI] [PubMed] [Google Scholar]
  38. Schmidt K. G., Ulmer H. E., Silverman N. H., Kleinman C. S., Copel J. A. Perinatal outcome of fetal complete atrioventricular block: a multicenter experience. J Am Coll Cardiol. 1991 May;17(6):1360–1366. doi: 10.1016/s0735-1097(10)80148-2. [DOI] [PubMed] [Google Scholar]
  39. Scott J. S., Maddison P. J., Taylor P. V., Esscher E., Scott O., Skinner R. P. Connective-tissue disease, antibodies to ribonucleoprotein, and congenital heart block. N Engl J Med. 1983 Jul 28;309(4):209–212. doi: 10.1056/NEJM198307283090403. [DOI] [PubMed] [Google Scholar]
  40. Sholler G. F., Walsh E. P. Congenital complete heart block in patients without anatomic cardiac defects. Am Heart J. 1989 Dec;118(6):1193–1198. doi: 10.1016/0002-8703(89)90009-4. [DOI] [PubMed] [Google Scholar]
  41. Taylor P. V., Scott J. S., Gerlis L. M., Esscher E., Scott O. Maternal antibodies against fetal cardiac antigens in congenital complete heart block. N Engl J Med. 1986 Sep 11;315(11):667–672. doi: 10.1056/NEJM198609113151103. [DOI] [PubMed] [Google Scholar]
  42. Waltuck J., Buyon J. P. Autoantibody-associated congenital heart block: outcome in mothers and children. Ann Intern Med. 1994 Apr 1;120(7):544–551. doi: 10.7326/0003-4819-120-7-199404010-00003. [DOI] [PubMed] [Google Scholar]
  43. Winkler R. B., Freed M. D., Nadas A. S. Exercise-induced ventricular ectopy in children and young adults with complete heart block. Am Heart J. 1980 Jan;99(1):87–92. doi: 10.1016/0002-8703(80)90317-8. [DOI] [PubMed] [Google Scholar]

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