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The Journal of Headache and Pain logoLink to The Journal of Headache and Pain
. 2008 Oct 25;10(1):51–53. doi: 10.1007/s10194-008-0079-x

CADASIL presenting as status migrainosus and persisting aura without infarction

Simona Sacco 1, Maurizia Rasura 2, Marina Cao 2, Alessandro Bozzao 3, Antonio Carolei 1,
PMCID: PMC3451763  PMID: 18953486

Abstract

Different types of migraine have been reported in 20–40% of patients with cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL). We describe a novel migrainous manifestation of CADASIL consisting in status migrainosus and persistent aura without infarction. The symptoms resolved after i.v. treatment with lorazepam and mannitol.

Keywords: CADASIL, Migraine, Aura, Headache, Triptans, International Classification of Headache Disorders

Full Text

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Conflict of interest

None.

Glossary

CADASIL

Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy

MRI

Magnetic resonance imaging

ICHD-2

International Classification of Headache Disorders, Second Edition

References

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