Abstract
Different types of migraine have been reported in 20–40% of patients with cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL). We describe a novel migrainous manifestation of CADASIL consisting in status migrainosus and persistent aura without infarction. The symptoms resolved after i.v. treatment with lorazepam and mannitol.
Keywords: CADASIL, Migraine, Aura, Headache, Triptans, International Classification of Headache Disorders
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Conflict of interest
None.
Glossary
- CADASIL
Cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy
- MRI
Magnetic resonance imaging
- ICHD-2
International Classification of Headache Disorders, Second Edition
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