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Indian Journal of Otolaryngology and Head & Neck Surgery logoLink to Indian Journal of Otolaryngology and Head & Neck Surgery
. 2007 Sep 14;59(2):178–181. doi: 10.1007/s12070-007-0054-x

Extranodal manifestation of Rosai Dorfman Disease of the nasopharynx

T Ramadass 1,✉, P Das Thulasi 1, N Geetha 2, Nithya Narayanan 1, Gopi Ayyaswamy 1, S Swapna 1
PMCID: PMC3451790  PMID: 23120426

Abstract

The aim of presenting this case is to highlight the fact that extranodal manifestation of Rosai Dorfman Disease (RDD) without lymphadenopathy was seen in a teenaged girl with recurrent episodes of epistaxis, due to a lobulated mass in the nasopharynx, which mimicked malignancy. This case is a rare presentation because the extranodal manifestation of RDD in multisystem organs are reported in literature, but the nasopharyngeal manifestation without lymphadenopathy is unique. The clinical presentation and surgical management of the case by endoscopic sinus surgery, the aetiopathology, differential diagnosis and review of literature are described here.

Keywords: Sinus histiocytosis with massive lympadenopathy [SHML], Rosai-Dorfman disease [R.D.D], Lymphoma Rhinoscleroma

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