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. 1985 Jan;40(1):23–26. doi: 10.1136/thx.40.1.23

Newly diagnosed cystic fibrosis in middle and later life.

B Hunt, D M Geddes
PMCID: PMC459972  PMID: 3918355

Abstract

Four patients with cystic fibrosis diagnosed in middle and later life are presented. All had chronic bronchopulmonary infection with a high sweat sodium concentration, and chest radiographic evidence of upper zone bronchiectasis. Two patients had pancreatic dysfunction. Sputum culture grew mucoid Pseudomonas aeruginosa in three patients and Haemophilus influenzae in one. Ages at diagnosis were 63, 42, 40, and 35 years. These patients confirm the possibility of occasional longevity in cystic fibrosis and emphasise the need to consider the diagnosis at all ages. They also provide encouragement for younger patients.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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