Skip to main content
NCBI home page
Thorax logoLink to Thorax
. 1990 Feb;45(2):122–125. doi: 10.1136/thx.45.2.122

Diagnosis of congenital cystic adenomatoid malformation of the lung in newborn infants and children.

H A Heij 1, S Ekkelkamp 1, A Vos 1
PMCID: PMC462322  PMID: 2315874

Abstract

Seventeen patients were diagnosed as having congenital cystic adenomatoid malformation of the lung during 1970-88. One case was associated with congenital diaphragmatic hernia and the child died before operation. The other 16 children underwent successful surgery. The patients presented in one of three ways--with neonatal respiratory impairment (12 cases) requiring urgent diagnosis and treatment, with recurrent respiratory tract infections (3), and with pneumothorax (1). Diagnostic problems arose with the neonatal presentation. In four of the children laparotomy was performed for presumed diaphragmatic hernia; three of these children had right sided lesions. Congenital diaphragmatic hernia was excluded by contrast studies in a further two patients. Histological examination confirmed the diagnosis in all cases. The postoperative course was uneventful in all 16 patients. No long term impairment of pulmonary function was noted.

Full text

PDF
122

Images in this article

123Image
on p.123
123Image
on p.123
123Image
on p.123

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Adzick N. S., Harrison M. R., Glick P. L., Golbus M. S., Anderson R. L., Mahony B. S., Callen P. W., Hirsch J. H., Luthy D. A., Filly R. A. Fetal cystic adenomatoid malformation: prenatal diagnosis and natural history. J Pediatr Surg. 1985 Oct;20(5):483–488. doi: 10.1016/s0022-3468(85)80470-x. [DOI] [PubMed] [Google Scholar]
  2. Ekkelkamp S., Vos A. Congenital cystic adenomatoid malformation of the lung: an unusual presentation. Z Kinderchir. 1987 Aug;42(4):253–254. doi: 10.1055/s-2008-1075598. [DOI] [PubMed] [Google Scholar]
  3. Hartenberg M. A., Brewer W. H. Cystic adenomatoid malformation of the lung: identification by sonography. AJR Am J Roentgenol. 1983 Apr;140(4):693–694. doi: 10.2214/ajr.140.4.693. [DOI] [PubMed] [Google Scholar]
  4. Miller R. K., Sieber W. K., Yunis E. J. Congenital adenomatoid malformation of the lung. A report of 17 cases and review of the literature. Pathol Annu. 1980;15(Pt 1):387–402. [PubMed] [Google Scholar]
  5. Nishibayashi S. W., Andrassy R. J., Woolley M. M. Congenital cystic adenomatoid malformation: 1 30-year experience. J Pediatr Surg. 1981 Oct;16(5):704–706. doi: 10.1016/s0022-3468(81)80556-8. [DOI] [PubMed] [Google Scholar]
  6. Rodgers B. M., Harman P. K., Johnson A. M. Bronchopulmonary foregut malformations. The spectrum of anomalies. Ann Surg. 1986 May;203(5):517–524. doi: 10.1097/00000658-198605000-00011. [DOI] [PMC free article] [PubMed] [Google Scholar]
  7. Ryckman F. C., Rosenkrantz J. G. Thoracic surgical problems in infancy and childhood. Surg Clin North Am. 1985 Dec;65(6):1423–1454. doi: 10.1016/s0039-6109(16)43781-3. [DOI] [PubMed] [Google Scholar]
  8. Ueda K., Gruppo R., Unger F., Martin L., Bove K. Rhabdomyosarcoma of lung arising in congenital cystic adenomatoid malformation. Cancer. 1977 Jul;40(1):383–388. doi: 10.1002/1097-0142(197707)40:1<383::aid-cncr2820400154>3.0.co;2-2. [DOI] [PubMed] [Google Scholar]

Articles from Thorax are provided here courtesy of BMJ Publishing Group

RESOURCES