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. 1992 Nov;47(11):988–990. doi: 10.1136/thx.47.11.988

Idiopathic pulmonary haemosiderosis: a form of microscopic polyarteritis?

B Leaker 1, G Cambridge 1, R M du Bois 1, G H Neild 1
PMCID: PMC464129  PMID: 1465763

Abstract

Idiopathic pulmonary haemosiderosis remains a diagnosis of exclusion in patients who present with pulmonary alveolar haemorrhage. Systemic vasculitis developed in a patient with an eight year history of idiopathic pulmonary haemosiderosis. The diagnosis was confirmed by a rising titre of antineutrophil cytoplasmic antibodies directed against myeloperoxidase. Treatment with immunosuppressive agents resulted in complete resolution of symptoms and suppression of the antibodies. Measurement of antineutrophil cytoplasmic antibodies is recommended for all patients with pulmonary alveolar haemorrhage syndromes.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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