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. 1977 Apr;32(2):140–148. doi: 10.1136/thx.32.2.140

A case of pulmonary veno-occlusive disease respondong to treatment with azathioprine.

J E Sanderson, S G Spiro, A T Hendry, M Turner-Warwick
PMCID: PMC470549  PMID: 867325

Abstract

Histological features of a lung biopsy specimen from a 46-year-old woman showed all the characteristics described in veno-occlusive disease. The clinical features, however, were distinctive in that in addition to the lung involvement there was alopecia, digital vasculitic ulcers, Raynaud's phenomenon, polyarthritis, and muscle weakness. Treatment with azathioprine resulted in a progressive improvement in her condition. It is suggested that pulmonary small vein occlusion may occur as a pattern of tissue response in more than one situation and that is sometimes more amenable to therapy than has been previously reported.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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