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. 1978 Feb;33(1):101–105. doi: 10.1136/thx.33.1.101

Familial combined cellular and humoral immune defect with multisystem granulomata.

W H Perks, I S Petheram
PMCID: PMC470855  PMID: 644530

Abstract

A brother and sister presented with recurrent respiratory infections. Investigations showed combined cellular and humoral immune defects and non-caseating granulomata in lungs, liver, lymph nodes, and skin. Despite antimycobacterial chemotherapy and corticosteroids in the brother and the additional treatment of human immunoglobulin injections in the sister both patients deteriorated with pulmonary and hepatic involvement.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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