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. 1971 Jul;26(4):365–375. doi: 10.1136/thx.26.4.365

Chronic idiopathic pulmonary hilar fibrosis

A clinicopathological entity

Magdi H Yacoub 1,1, Vernon C Thompson 1
PMCID: PMC472312  PMID: 5565782

Abstract

Idiopathic pulmonary hilar fibrosis is a condition related to mediastinal fibrosis, characterized by localization of the fibrosing process to one or both pulmonary hila. This results in pulmonary hypertension and bronchial narrowing. Three patients suffering from this disease, in whom the diagnosis has been confirmed by thoracotomy, are reported. The clinical and pathological features are described and previously reported cases are reviewed. The syndrome is classified into two types, according to whether the obstruction affects mainly the pulmonary artery or veins. The disease is a self-limiting one but may lead to organic changes in the lungs causing severe disability.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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