Abstract
Interruption of the aortic arch is an uncommon malformation in which there is no direct continuity between the aortic arch and the descending aorta, the latter arising through a patent ductus arteriosus. Three types are described, depending upon the site of interruption in relation to the arch vessels. A large ventricular septal defect is present in 94% of cases. It is to be distinguished from aortic arch atresia, which should be regarded as a severe form of preductal coarctation in which the luminal continuity of the arch and descending aorta is absent. Three cases are described: the first demonstrates the natural outcome of the uncorrected anomaly with progression to Eisenmenger's syndrome; the second illustrates the feasibility of surgical treatment in the neonate; the third is an example of total correction of aortic arch interruption with the common associated anomalies. Diagnosis in infancy is difficult in view of the paucity of definite clinical criteria. Surgery in the infant should consist of reconstruction of the aortic arch together with pulmonary artery banding. In older children total correction can usually be performed electively in a two-stage procedure.
Full text
PDF
Images in this article
Selected References
These references are in PubMed. This may not be the complete list of references from this article.
- CELORIA G. C., PATTON R. B. Congenital absence of the aortic arch. Am Heart J. 1959 Sep;58:407–413. doi: 10.1016/0002-8703(59)90157-7. [DOI] [PubMed] [Google Scholar]
- DAVES M. L., TREGER A. VERTEBRAL GRAND LARCENY. Circulation. 1964 Jun;29:911–913. doi: 10.1161/01.cir.29.6.911. [DOI] [PubMed] [Google Scholar]
- EVERTS-SUAREZ E. A., CARSON C. P. The triad of congenital absence of aortic arch (isthmus aortae), patent ductus arteriosus and interventricular septal defect; a trilogy. Ann Surg. 1959 Jul;150(1):153–159. doi: 10.1097/00000658-195907000-00019. [DOI] [PMC free article] [PubMed] [Google Scholar]
- FOURNIER P., ZAIDI Z. H. Congenital absence of the aortic arch. Am Heart J. 1960 Jan;59:148–152. doi: 10.1016/0002-8703(60)90394-x. [DOI] [PubMed] [Google Scholar]
- Hairston P., Webb H., Lee W. H., Jr Aortic arch interruption: treatment with pulmonary artery banding. J Thorac Cardiovasc Surg. 1967 Jul;54(1):60–64. [PubMed] [Google Scholar]
- Lie J. T. The malformation complex of the absence of the arch of the aorta--Steidele's complex. Am Heart J. 1967 May;73(5):615–625. doi: 10.1016/0002-8703(67)90171-8. [DOI] [PubMed] [Google Scholar]
- PILLSBURY R. C., LOWER R. R., SHUMWAY N. E. ATRESIA OF THE AORTIC ARCH. Circulation. 1964 Nov;30:749–754. doi: 10.1161/01.cir.30.5.749. [DOI] [PubMed] [Google Scholar]
- REIDBORD H. E. COMPLETE INTERRUPTION OF THE AORTIC ARCH. REPORT OF A CASE. J Lancet. 1964 Oct;84:339–342. [PubMed] [Google Scholar]
- ROBERTS W. C., MORROW A. G., BRAUNWALD E. Complete interruption of the aortic arch. Circulation. 1962 Jul;26:39–59. doi: 10.1161/01.cir.26.1.39. [DOI] [PubMed] [Google Scholar]
- Rochette M., Stanley P., F-Ethier M., Davignon A. Complete interruption of the aortic arch in infancy. Can Med Assoc J. 1968 Jan 20;98(3):131–139. [PMC free article] [PubMed] [Google Scholar]
- Singh M. P., Bentall H. H., Oakley C. M. Successful total correction of congenital interruption of the aortic arch and ventricular septal defect. Thorax. 1970 Sep;25(5):615–623. doi: 10.1136/thx.25.5.615. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Tawes R. L., Jr, Panagopoulos P., Aberdeen E., Waterston D. J., Bonham-Carter R. E. Aortic arch atresia and interreuption of the aortic arch. Experience in 11 cases of operation. J Thorac Cardiovasc Surg. 1969 Oct;58(4):492–501. [PubMed] [Google Scholar]
- Tyson K. R., Harri L. C., Ngiem Q. X. Repair of aortic arch interruption in the neonate. Surgery. 1970 Jun;67(6):1006–1010. [PubMed] [Google Scholar]