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. 1973 Sep;26(9):678–683. doi: 10.1136/jcp.26.9.678

Enzymes involved in phenylalanine metabolism in the human foetus and child

Anne McLean 1,2, Margaret J Marwick 1,2, Barbara E Clayton 1,2
PMCID: PMC477849  PMID: 4148075

Abstract

The activities of phenylalanine p-hydroxylase, tyrosine: alpha-ketoglutarate and phenylalanine: pyruvate aminotransferases, and aromatic alpha-ketoacid reductase have been measured in liver biopsies obtained from children with a series of disorders other than phenylketonuria and from human foetuses aged 8·5 to 24 weeks. The importance of such a study in relation to the management of infants with hyperphenylalaninaemia and pregnant phenylketonuric women is discussed

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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