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. 1964 Mar;17(2):135–142. doi: 10.1136/jcp.17.2.135

Congenital hepatic fibrosis with an unusual pulmonary lesion

Roger Williams 1,2,3, Peter J Scheuer 1,2,3, Brian E Heard 1,2,3
PMCID: PMC480703  PMID: 14149937

Abstract

The necropsy findings in a 5-year-old girl with congenital hepatic fibrosis are described. She had been followed since the age of 18 months and finally developed hepatocellular failure. Extensive haemorrhagic necrosis was found at necropsy and was probably related to the terminal illness. Other unusual findings were areas of typical post-necrotic cirrhosis and marked centrilobular and diffuse emphysema of the lungs. It is suggested that the latter was also congenital in origin.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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