Abstract
A 3-day-old infant investigated for cyanotic heart disease was found to have partial DiGeorge syndrome and pulmonary atresia with ventricular septal defect. The only source of pulmonary blood flow was a right-sided persistent ductus arteriosus which originated from an aberrant right subclavian artery. Such a vascular ring has not been described previously. Surgical treatment included a left-sided prosthetic shunt in infancy followed by resection of the ligamentum arteriosum and right subclavian artery during the second year of life.
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- Arciniegas E., Hakimi M., Hertzler J. H., Farooki Z. Q., Green E. W. Surgical management of congenital vascular rings. J Thorac Cardiovasc Surg. 1979 May;77(5):721–727. [PubMed] [Google Scholar]
- BAHNSON H. T., BLALOCK A. Aortic vascular rings encountered in the surgical treatment of congenital pulmonic stenosis. Ann Surg. 1950 Mar;131(3):356–362. doi: 10.1097/00000658-195003000-00006. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Baumstark A. E., Gordon D. H., Haller J. O., Martin E. C. The left aortic arch and right descending aorta. Br J Radiol. 1977 Nov;50(599):788–792. doi: 10.1259/0007-1285-50-599-788. [DOI] [PubMed] [Google Scholar]
- Berman W., Jr, Yabek S. M., Dillon T., Neal J. F., Akl B., Burstein J. Vascular ring due to left aortic arch and right descending aorta. Circulation. 1981 Feb;63(2):458–460. doi: 10.1161/01.cir.63.2.458. [DOI] [PubMed] [Google Scholar]
- Binet J. P., Carpentier J., Pottemain M., Langlois J. Double aortic arch associated with tetralogy of Fallot in infants; report of two cases. J Thorac Cardiovasc Surg. 1966 Jan;51(1):116–118. [PubMed] [Google Scholar]
- Conley M. E., Beckwith J. B., Mancer J. F., Tenckhoff L. The spectrum of the DiGeorge syndrome. J Pediatr. 1979 Jun;94(6):883–890. doi: 10.1016/s0022-3476(79)80207-3. [DOI] [PubMed] [Google Scholar]
- Ergin M. A., Jayaram N., LaCorte M. Left aortic arch and right descending aorta: diagnostic and therapeutic implications of a rare type of vascular ring. Ann Thorac Surg. 1981 Jan;31(1):82–85. doi: 10.1016/s0003-4975(10)61323-9. [DOI] [PubMed] [Google Scholar]
- Freedom R. M., Rosen F. S., Nadas A. S. Congenital cardiovascular disease and anomalies of the third and fourth pharyngeal pouch. Circulation. 1972 Jul;46(1):165–172. doi: 10.1161/01.cir.46.1.165. [DOI] [PubMed] [Google Scholar]
- Miller M. J., Frame B. Partial DiGeorge syndrome or branchial dysembryogenesis. Am J Dis Child. 1976 Dec;130(12):1376–1377. doi: 10.1001/archpedi.1976.02120130082023. [DOI] [PubMed] [Google Scholar]
- Moerman P., Goddeeris P., Lauwerijns J., Van der Hauwaert L. G. Cardiovascular malformations in DiGeorge syndrome (congenital absence of hypoplasia of the thymus). Br Heart J. 1980 Oct;44(4):452–459. doi: 10.1136/hrt.44.4.452. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Park S. C., Siewers R. D., Neches W. H., Lenox C. C., Zuberbuhler J. R. Left aortic arch with right descending aorta and right ligamentum arteriosum. A rare form of vascular ring. J Thorac Cardiovasc Surg. 1976 May;71(5):779–784. [PubMed] [Google Scholar]
- Waterston D. J., Pohl V., Kallfelz H. C., Kreutzberg B. Shuntoperationen bei Fallotscher Tetralogie mit doppeltem Aortenbogen. Dtsch Med Wochenschr. 1971 Jul 9;96(28):1191–1195. doi: 10.1055/s-0028-1110105. [DOI] [PubMed] [Google Scholar]
- de Leval M. R., McKay R., Jones M., Stark J., Macartney F. J. Modified Blalock-Taussig shunt. Use of subclavian artery orifice as flow regulator in prosthetic systemic-pulmonary artery shunts. J Thorac Cardiovasc Surg. 1981 Jan;81(1):112–119. [PubMed] [Google Scholar]