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. 1983 Dec;50(6):586–589. doi: 10.1136/hrt.50.6.586

Absent pulmonary valve syndrome. Surgical correction with pulmonary arterioplasty.

P S Rao, G M Lawrie
PMCID: PMC481464  PMID: 6652001

Abstract

A 13 month old child with classic features of absent pulmonary valve with tetralogy of Fallot underwent successful surgical repair by closure of the ventricular septal defect, relief of the right ventricular outflow tract obstruction, and partial resection and plastic repair of the aneurysmally dilated pulmonary arteries. Cardiac catheterisation data and clinical follow up for more than 18 months after the operation indicated excellent results. It is suggested that plastic repair of the aneurysmally dilated pulmonary arteries along with closure of the ventricular septal defect and relief of the right ventricular outflow tract obstruction should be performed early, perhaps between 1 and 2 years of age.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. Bove E. L., Shaher R. M., Alley R., McKneally M. Tetralogy of Fallot with absent pulmonary valve and aneurysm of the pulmonary artery: report of two cases presenting as obstructive lung disease. J Pediatr. 1972 Aug;81(2):339–343. doi: 10.1016/s0022-3476(72)80307-x. [DOI] [PubMed] [Google Scholar]
  2. CORTES F. M., JACOBY W. J. Isolated congenital pulmonary valvular insufficiency. Am J Cardiol. 1962 Aug;10:287–290. doi: 10.1016/0002-9149(62)90310-7. [DOI] [PubMed] [Google Scholar]
  3. Ellison R. G., Brown W. J., Jr, Yeh T. J., Hamilton W. F. Surgical significance of acute and chronic pulmonary valvular insufficiency. J Thorac Cardiovasc Surg. 1970 Oct;60(4):549–558. [PubMed] [Google Scholar]
  4. Finnegan P., Haider R., Patel R. G., Abrams L. S., Singh S. P. Results of total correction of the tetralogy of Fallot. Long-term haemodynamic evaluation at rest and during exercise. Br Heart J. 1976 Sep;38(9):934–942. doi: 10.1136/hrt.38.9.934. [DOI] [PMC free article] [PubMed] [Google Scholar]
  5. Geha A. S., Laks H., Stansel H. C., Jr, Cornhill J. F., Kilman J. W., Buckley M. J., Roberts W. C. Late failure of porcine valve heterografts in children. J Thorac Cardiovasc Surg. 1979 Sep;78(3):351–364. [PubMed] [Google Scholar]
  6. HOSIER D. M., PITTS J. L., TAUSSIG H. B. Results of valvulotomy for valvular pulmonary stenosis with intact ventricular septum; analysis of sixty-nine patients. Circulation. 1956 Jul;14(1):9–16. doi: 10.1161/01.cir.14.1.9. [DOI] [PubMed] [Google Scholar]
  7. Ilbawi M. N., Idriss F. S., Muster A. J., Wessel H. U., Paul M. H., DeLeon S. Y. Tetralogy of Fallot with absent pulmonary valve. Should valve insertion be part of the intracardiac repair? J Thorac Cardiovasc Surg. 1981 Jun;81(6):906–915. [PubMed] [Google Scholar]
  8. Ilbawi M. N., Idriss F. S., Muster A. J., Wessel H. U., Paul M. H., DeLeon S. Y. Tetralogy of Fallot with absent pulmonary valve. Should valve insertion be part of the intracardiac repair? J Thorac Cardiovasc Surg. 1981 Jun;81(6):906–915. [PubMed] [Google Scholar]
  9. Litwin S. B., Rosenthal A., Fellows K. Surgical management of young infants with tetralogy of Fallot, absence of the pulmonary valve, and respiratory distress. J Thorac Cardiovasc Surg. 1973 Apr;65(4):552–558. [PubMed] [Google Scholar]
  10. Miller D. C., Rossiter S. J., Stinson E. B., Oyer P. E., Reitz B. A., Shumway N. E. Late right heart reconstruction following repair of tetralogy of Fallot. Ann Thorac Surg. 1979 Sep;28(3):239–251. doi: 10.1016/s0003-4975(10)63113-x. [DOI] [PubMed] [Google Scholar]
  11. Osman M. Z., Meng C. C., Girdany B. R. Congenital absence of the pulmonary valve: report of eight cases with review of the literature. Am J Roentgenol Radium Ther Nucl Med. 1969 May;106(1):58–69. doi: 10.2214/ajr.106.1.58. [DOI] [PubMed] [Google Scholar]
  12. Pinsky W. W., Nihill M. R., Mullins C. E., Harrison G., McNamara D. G. The absent pulmonary valve syndrome. Considerations of management. Circulation. 1978 Jan;57(1):159–162. doi: 10.1161/01.cir.57.1.159. [DOI] [PubMed] [Google Scholar]
  13. Waldhausen J. A., Friedman S., Nicodemus H., Miller W. W., Rashkind W., Johnson J. Absence of the pulmonary valve in patients with tetralogy of Fallot. Surgical management. J Thorac Cardiovasc Surg. 1969 May;57(5):669–674. [PubMed] [Google Scholar]

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