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. 1984 Aug;52(2):233–236. doi: 10.1136/hrt.52.2.233

Primary cardiac amyloidosis in a young man presenting with angina pectoris.

S Saltissi, P J Kertes, D G Julian
PMCID: PMC481616  PMID: 6743441

Abstract

A 32 year old man presenting with typical angina pectoris was found to have primary cardiac amyloidosis. Myocardial infiltration was strongly suggested by echocardiography, and a histological diagnosis was confirmed by renal biopsy. Nevertheless, technetium pyrophosphate myocardial scanning, recently proposed as a sensitive non-invasive test, showed negative results despite widespread cardiac involvement confirmed at necropsy after unexpected sudden death. Postmortem findings also showed subintimal amyloid material in a severely narrowed right coronary artery. This case highlights several unusual clinical features in a patient with advanced primary cardiac amyloidosis.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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