Abstract
The lung was biopsied in 20 children with double inlet ventricle and pulmonary hypertension aged 2 months to 14 years. Eleven patients had two patent atrioventricular valves, three atresia of the right valve, and six hypoplasia of the left valve. Severe pulmonary arterial medial hypertrophy occurred in the nine children less than 1 year of age. The findings did not suggest a period of normality after birth when the pulmonary artery might have been banded most effectively. Of the 11 older patients, eight had medial hypertrophy and three intimal proliferation with medial atrophy. Six patients with medial hypertrophy had some reduction in pulmonary arterial pressure after banding. It is recommended that the pulmonary artery be banded as early as possible, and rebanded early if a satisfactory result is not obtained, particularly in patients destined for a Fontan-Kreutzer procedure. Early atrial septectomy should reduce the arterial and venous abnormalities seen in left atrioventricular valve hypoplasia.
Full text
PDF
Selected References
These references are in PubMed. This may not be the complete list of references from this article.
- Freedom R. M., Sondheimer H., Sische R., Rowe R. D. Development of "subaortic stenosis" after pulmonary arterial banding for common ventricle. Am J Cardiol. 1977 Jan;39(1):78–83. doi: 10.1016/s0002-9149(77)80015-5. [DOI] [PubMed] [Google Scholar]
- Haworth S. G., Hislop A. A. Pulmonary vascular development: normal values of peripheral vascular structure. Am J Cardiol. 1983 Sep 1;52(5):578–583. doi: 10.1016/0002-9149(83)90030-9. [DOI] [PubMed] [Google Scholar]
- Hislop A., Reid L. New pathological findings in emphysema of childhood. 1. Polyalveolar lobe with emphysema. Thorax. 1970 Nov;25(6):682–690. doi: 10.1136/thx.25.6.682. [DOI] [PMC free article] [PubMed] [Google Scholar]
- Kreutzer G., Schlichter A., Laura J. P., Suárez J. C., Vargas J. F. Univentricular heart with low pulmonary vascular resistances: septation vs atriopulmonary anastomosis. Arq Bras Cardiol. 1981 Oct;37(4):301–307. [PubMed] [Google Scholar]
- Stefanelli G., Kirklin J. W., Naftel D. C., Blackstone E. H., Pacifico A. D., Kirklin J. K., Soto B., Bargeron L. M., Jr Early and intermediate-term (10-year) results of surgery for univentricular atrioventricular connection ("single ventricle"). Am J Cardiol. 1984 Oct 1;54(7):811–821. doi: 10.1016/s0002-9149(84)80213-1. [DOI] [PubMed] [Google Scholar]
- Villani M., Crupi G., Locatelli G., Tiraboschi R., Vanini V., Parenzan L. Experience in palliative treatment of univentricular heart including tricuspid atresia. Herz. 1979 Apr;4(2):256–261. [PubMed] [Google Scholar]