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. 1983 Dec;46(12):1143–1145. doi: 10.1136/jnnp.46.12.1143

Studies of cellular radiosensitivity in hereditary disorders of nervous system and muscle.

S Brennan, P D Lewis
PMCID: PMC491782  PMID: 6663314

Abstract

Skin fibroblasts from patients with familial dysautonomia, Duchenne muscular dystrophy and Charcot-Marie-Tooth disease show normal sensitivity to ionising radiation, as measured by post-irradiation clonal growth. Previous reports of cellular hypersensitivity to ionising radiation and other DNA-damaging agents in familial dysautonomia and Duchenne muscular dystrophy have not been confirmed.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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