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. 1973 Oct;36(5):769–776. doi: 10.1136/jnnp.36.5.769

Intracranial reticulum cell sarcoma associated with immunoglobulin A deficiency

M C Gregory 1,2,1, J T Hughes 1,2
PMCID: PMC494455  PMID: 4356731

Abstract

A case is reported of a 46 year old woman who died after a five month illness characterized by focal neurological signs, evidence of meningeal irritation, and the finding of `blast' cells in the CSF. Immunoglobulin A was consistently absent from her serum and secretions. Necropsy showed extensive infiltration by a reticulum-cell sarcoma of the subarachnoid space, with tumour nodules on several cranial nerves and tumour infiltration of the tuber cinereum. The significance of the association between immunoglobulin A deficiency and neoplasia is discussed.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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