Table 1.
Subject demographics, organ involvements, pulmonary function tests
| Patients | Controls | |
|---|---|---|
| Age years | 44.4 ± 11 | 40.6 ± 11.8 |
| BMI (kg m−2) | 31.9 ± 5.2 | 31.0 ± 7.1 |
| Gender [N (%)] | ||
| Male | 6 (30) | 5 (30) |
| Female | 14 (70) | 12 (70) |
| Race [N (%)] | ||
| African American | 20 (100) | 17 (100) |
| Smoking status | ||
| Yes | 3 (15) | 0 (0) |
| No | 17 (85) | 17 (100) |
| Organ involvement | ||
| Lung | 20 (100) | N/A |
| Skin | 12 (60) | |
| Eye | 7 (35) | |
| Multi-organ | 19 (99) | |
| PFT values | ||
| FEV1 % | 88 (5.7) | N/A |
| FVC % | 95 (4.5) | N/A |
| Baseline O2 saturation | 98 (0.37) | N/A |
Results are reported as mean ± SEM
N (%) number of subjects and percent given in parentheses, BMI body mass index, PFT pulmonary function test, FEV1 % percent predicted forced expiratory volume, FVC % percent predicted forced vital capacity