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. 1994 Jun;78(6):430–432. doi: 10.1136/bjo.78.6.430

Dark adaptation in patients with Best vitelliform macular dystrophy.

W Baca 1, G A Fishman 1, K R Alexander 1, A M Glenn 1
PMCID: PMC504815  PMID: 8060924

Abstract

Psychophysical dark adaptation studies were performed in six patients with Best vitelliform macular dystrophy (BVMD) using a Goldmann-Weekers dark adaptometer. Prebleach thresholds were determined before obtaining a postbleach full recovery curve. Unlike patients with Stargardt macular dystrophy, all patients with BVMD showed a normal time to reach their baseline dark adapted thresholds after bleaching of their rod visual pigment when tested in clinically normal appearing retina. Although a lipofuscin material accumulates within retinal pigment epithelial cells in patients with either Best or Stargardt dystrophy, functional findings pertaining to recovery of rod dark adaptation thresholds as well as electro-oculogram light peak to dark trough ratios are different in these two disorders.

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Selected References

These references are in PubMed. This may not be the complete list of references from this article.

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