This article reports that PGC-1α improves mitochondrial myopathy and that its overexpression can compensate for an OXPHOS defect. Following an investigation of the first author, Dr. Wenz, by the University of Cologne, Germany, the university came to the conclusion that scientific misconduct was proven with respect to the above paper. Specifically, blot duplications were identified in Figures S3, S4, and S5. Given that the scientific integrity of the study has been compromised, we see the retraction of the paper as the best corrective action and sincerely apologize to the scientific community.