Skip to main content
Proceedings of the National Academy of Sciences of the United States of America logoLink to Proceedings of the National Academy of Sciences of the United States of America
. 1968 May;60(1):179–185. doi: 10.1073/pnas.60.1.179

The structure of acid mucopolysaccharides produced by Hurler fibroblasts in tissue culture.

R Matalon, A Dorfman
PMCID: PMC539099  PMID: 4232012

Full text

PDF
179

Selected References

These references are in PubMed. This may not be the complete list of references from this article.

  1. BARKER S. A., STACEY M. The pathology and chemistry of a case of gargoylism. Appendix. Chemical analysis of tissue polysaccharides. J Clin Pathol. 1956 Nov;9(4):314–315. [PubMed] [Google Scholar]
  2. BOAS N. F. Method for the determination of hexosamines in tissues. J Biol Chem. 1953 Oct;204(2):553–563. [PubMed] [Google Scholar]
  3. BRANTE G. Gargoylism; a mucopolysaccharidosis. Scand J Clin Lab Invest. 1952;4(1):43–46. doi: 10.3109/00365515209060631. [DOI] [PubMed] [Google Scholar]
  4. Brown D. H. TISSUE STORAGE OF MUCOPOLYSACCHARIDES IN HURLER-PFAUNDLER'S DISEASE. Proc Natl Acad Sci U S A. 1957 Sep 15;43(9):783–790. doi: 10.1073/pnas.43.9.783. [DOI] [PMC free article] [PubMed] [Google Scholar]
  5. DORFMAN A. METABOLISM OF ACID MUCOPOLYSACCHARIDES. Biophys J. 1964 Jan;4:SUPPL155–SUPPL165. doi: 10.1016/s0006-3495(64)86935-6. [DOI] [PMC free article] [PubMed] [Google Scholar]
  6. Danes B. S., Bearn A. G. Hurler's syndrome. A genetic study in cell culture. J Exp Med. 1966 Jan 1;123(1):1–16. doi: 10.1084/jem.123.1.1. [DOI] [PMC free article] [PubMed] [Google Scholar]
  7. Dorfman A., Lorincz A. E. OCCURRENCE OF URINARY ACID MUCOPOLYSACCHARIDES IN THE HURLER SYNDROME. Proc Natl Acad Sci U S A. 1957 Jun 15;43(6):443–446. doi: 10.1073/pnas.43.6.443. [DOI] [PMC free article] [PubMed] [Google Scholar]
  8. Fransson L. A., Rodén L. Structure of dermatan sulfate. I. Degradation by testicular hyaluronidase. J Biol Chem. 1967 Sep 25;242(18):4161–4169. [PubMed] [Google Scholar]
  9. Knecht J., Cifonelli J. A., Dorfman A. Structural studies on heparitin sulfate of normal and Hurler tissues. J Biol Chem. 1967 Oct 25;242(20):4652–4661. [PubMed] [Google Scholar]
  10. Knecht J., Dorfman A. Structure of heparitin sulfate in tissues of the Hurler syndrome. Biochem Biophys Res Commun. 1965 Dec 9;21(5):509–515. doi: 10.1016/0006-291x(65)90413-4. [DOI] [PubMed] [Google Scholar]
  11. LOWRY O. H., ROSEBROUGH N. J., FARR A. L., RANDALL R. J. Protein measurement with the Folin phenol reagent. J Biol Chem. 1951 Nov;193(1):265–275. [PubMed] [Google Scholar]
  12. MATHEWS M. B. Acid strength of carboxyl groups in isomeric chondroitin sulfates. Biochim Biophys Acta. 1961 Apr 1;48:402–403. doi: 10.1016/0006-3002(61)90494-2. [DOI] [PubMed] [Google Scholar]
  13. MATHEWS M. B., DORFMAN A. The molecular weight and viscosity of chondroitinsulfuric acid. Arch Biochem Biophys. 1953 Jan;42(1):41–53. doi: 10.1016/0003-9861(53)90235-5. [DOI] [PubMed] [Google Scholar]
  14. MATHEWS M. B., ROSEMAN S., DORFMAN A. Determination of the chondroitinase activity of bovine testicular preparations. J Biol Chem. 1951 Jan;188(1):327–334. [PubMed] [Google Scholar]
  15. MCKUSICK V. A. THE GENETIC MUCOPOLYSACCHARIDOSES. Circulation. 1965 Jan;31:1–4. doi: 10.1161/01.cir.31.1.1. [DOI] [PubMed] [Google Scholar]
  16. MEYER K., GRUMBACH M. M., LINKER A., HOFFMAN P. Excretion of sulfated mucopolysaccharides in gargoylism (Hurler's syndrome). Proc Soc Exp Biol Med. 1958 Feb;97(2):275–279. doi: 10.3181/00379727-97-23714. [DOI] [PubMed] [Google Scholar]
  17. MUIR H. The nature of the link between protein and carbohydrate of a chondroitin sulphate complex from hyaline cartilage. Biochem J. 1958 Jun;69(2):195–204. doi: 10.1042/bj0690195. [DOI] [PMC free article] [PubMed] [Google Scholar]
  18. Matalon R., Dorfman A. Hurler's syndrome: biosynthesis of acid mucopolysaccharides in tissue culture. Proc Natl Acad Sci U S A. 1966 Oct;56(4):1310–1316. doi: 10.1073/pnas.56.4.1310. [DOI] [PMC free article] [PubMed] [Google Scholar]
  19. PERLMAN R. L., TELSER A., DORFMAN A. THE BIOSYNTHESIS OF CHONDROITIN SULFATE BY A CELL-FREE PREPARATION. J Biol Chem. 1964 Nov;239:3623–3629. [PubMed] [Google Scholar]
  20. PETERSON E. A., GREENBERG D. M. Characteristics of the amino acid-incorporating system of liver homogenates. J Biol Chem. 1952 Jan;194(1):359–375. [PubMed] [Google Scholar]
  21. SCHILLER S., SLOVER G. A., DORFMAN A. A method for the separation of acid mucopolysaccharides: its application to the isolation of heparin from the skin of rats. J Biol Chem. 1961 Apr;236:983–987. [PubMed] [Google Scholar]
  22. Telser A., Robinson H. C., Dorfman A. The biosynthesis of chondroitin-sulfate protein complex. Proc Natl Acad Sci U S A. 1965 Sep;54(3):912–919. doi: 10.1073/pnas.54.3.912. [DOI] [PMC free article] [PubMed] [Google Scholar]

Articles from Proceedings of the National Academy of Sciences of the United States of America are provided here courtesy of National Academy of Sciences

RESOURCES