Table 2:

Natural history of hearing loss for all EVA ears^*

	Number of mutant alleles of SLC26A4
	M0	M1	M2	Total (M0 + M1 + M2)
Number of ears	72	20	15	107
Median duration of audiometric follow-up (y)	4.0	3.5	4.0	4.0
Mean (± s.d.) number of audiograms	8.1 (± 5.8)	6.8 (± 3.0)	8.9 (± 3.7)	8.0 (± 5.1)
Number (%) of ears with fluctuations in hearing	53 (74)	17 (85)	12 (80)	82 (77)
Number (%) of ears with stable hearing	8 (11)	1 (5)	1 (7)	10 (9)
Number (%) of ears with progressive hearing loss	11 (15)	2 (10)	2 (13)	15 (14)

^*excluding ears with any pure-tone average greater than 70 dBHL