Table 1:
Prevalence of Radiographic Extraskeletal Calcifications at Baseline (pre-treatment)
| Variable | Male (n= 16) | Female (n= 23) | All (n= 39) | |
|---|---|---|---|---|
| Age (years) | Mean ± SD (n) | 6.81 ± 4.29 (16) | 5.74 ± 3.24 (23) | 6.18 ± 3.69 (39) |
| Median (IQR) | 8.00 (3.00, 9.50) | 5.00 (3.00, 8.00) | 6.00 (3.00, 8.00) | |
| Calcium Deposit Seen on X-ray, n (%) | Yes | 3 (19) | 9 (39) | 12 (31) |
| No | 13 (81) | 14 (61) | 27 (69) | |
| Number of Ca Deposits, n (%) | 0 | 13 (81) | 14 (61) | 27 (69) |
| 1 | 2 (13) | 6 (26) | 8 (20.5) | |
| 2 | 0 (0) | 3 (13) | 3 (8) | |
| 3 | 1 (6) | 0 (0) | 1 (2.5) | |
| Area of largest Ca deposit (mm2) for positive patients | Mean ± sd (n) | 46.3 ± 70.7 (3) | 7.6 ± 6.8 (9) | 17.3 ± 35.4 (12) |
| Median (IQR) | 7.0 (4.0, 128.0) | 6.00 (3.6, 8.2) | 6.50 (3.8, 8.9) | |
| Location of largest Ca deposit for positive patients (n (%) | Tuft | 2 (12.5) | 8 (35) | 10 (26) |
| Abdomen | 0 (0) | 1 (4) | 1 (2.5) | |
| Tibia | 1 (6) | 0 (0) | 1 (2.5) | |